Gorlin-Goltz syndrome: A clinico radiological illustrative case report

Gorlin-Goltz syndrome is an infrequent multisystemic disease that is inherited in an autosomal dominant way showing a high level of penetrance & variable expressiveness. It is about a multisystemic process that is characterized by the presence of odontogenic keratocysts in the jaws, multiple basal cell nevi or carcinomas, palmar and/or plantar pits & calcification of falx cerebri. Diagnosis of Gorlin-Goltz syndrome is made by having two major criteria or one major & two minor criteria. Here, we report a case of a 11-year-old girl suffering from this syndrome presenting with two new entities namely bifid tongue & partial ankyloglossia.