Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; AHA; American Heart Association; aSCD; aborted sudden cardiac death; ATP; anti-tachycardia pacing; CMR; cardiovascular magnetic resonance scanning; CHD; coronary heart disease; CPVT; catecholaminergic polymorphic ventricular tachycardia; ECG; electrocardi
مقالات ISI تاکیکاردی بطنی پلی مورفید Catecholaminergic (ترجمه نشده)
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Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Idiopathic ventricular fibrillation; Genetics; Catecholaminergic polymorphic ventricular tachycardia; RYR2; Genetic testing;
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; coronary; dyslipidemia; failure; fibrillation; insurance; sudden death; AF; atrial fibrillation; ASCVD; atherosclerotic cardiovascular disease; BP; blood pressure; CPVT; catecholaminergic polymorphic ventricular tachycardia; D2B; door-to-balloon; HFpEF; h
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; ajmaline provocation testing; cardiomyopathy; ion channelopathy; sudden arrhythmic death syndrome; BrS; Brugada syndrome; CPVT; catecholaminergic polymorphic ventricular tachycardia; DCM; dilated cardiomyopathy; ARVC; arrhythmogenic right ventricular card
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Gene mutation; Induced pluripotent stem cell model; Inherited arrhythmia; Personalized medicine; AP; action potential; ARVC; arrhythmogenic right ventricular cardiomyopathy; BrS; Brugada syndrome; CPVT; catecholaminergic polymorphic ventricular tachycardi
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Subcutaneous defibrillator; Inappropriate shock delivery; Myopotential oversensing; Device repositioning; Catecholaminergic polymorphic ventricular tachycardia;
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Syncope; Inherited arrhythmia; Long QT syndrome; Brugada syndrome; Catecholaminergic polymorphic ventricular tachycardia;
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; AP; action potential; APD; action potential duration; CPVT; catecholaminergic polymorphic ventricular tachycardia; CamKII; calcium calmodulin dependent kinase II; ERP; effective refractory period; ICD; implantable cardiac defibrillator; “Ix” where x i
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; ACM; arrhythmogenic cardiomyopathy; ACMG; American College of Medical Genetics and Genomics; AF; atrial fibrillation; BrS; Brugada syndrome; CHD; coronary heart disease; CPVT; catecholaminergic polymorphic ventricular tachycardia; CVD; cardiovascular dise
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Catecholaminergic polymorphic ventricular tachycardia; Thoracoscopic bilateral sympathectomy; Implantable cardioverter defibrillator
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; sudden cardiac arrest; family history; patient history; hypertrophic cardiomyopathy; long QT syndrome; catecholaminergic polymorphic ventricular tachycardia; congenital coronary artery anomalies; AAP; American Academy of Pediatrics; ALCA-R; Anomalous orig
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Atrial fibrillation; Channelopathy; Brugada syndrome; Long QT syndrome; Short QT syndrome; Catecholaminergic polymorphic ventricular tachycardia
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Ventricular tachycardia; Ventricular fibrillation; Exercise; Arrhythmogenic right ventricular cardiomyopathy; Mitral valve prolapse; Catecholaminergic polymorphic ventricular tachycardia;
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Long QT syndrome; Brugada syndrome; Catecholaminergic polymorphic ventricular tachycardia; Cardiomyopathy; Hypertrophic; Arrhythmogenic right ventricular dysplasia; Exercise; Sudden cardiac death;
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; ARVD/C; arrhythmogenic right ventricular dysplasia/cardiomyopathy; BrS; Brugada syndrome; CHD; coronary heart disease; CPVT; catecholaminergic polymorphic ventricular tachycardia; DCM; dilated cardiomyopathy; GWAS; genome wide association study; HCM; hype
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; ACMG; American College of Medical Genetics and Genomics; CPVT; catecholaminergic polymorphic ventricular tachycardia; ECG; electrocardiogram; ExAC; Exome Aggregation Consortium; HCM; hypertrophic cardiomyopathy; INDEL; insertion/deletion; LOF; loss of fun
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; ACMG; American College of Medical Genetics; AF; familial atrial fibrillation; BrS; Brugada syndrome; CCS; cardiac conduction system; CPVT; catecholaminergic polymorphic ventricular tachycardia; ECG; electrocardiogram; LQTS; long QT syndrome; SCD; sudden
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; AHA; American Heart Association; ARVC; arrhythmogenic right ventricular cardiomyopathy; BrS; Brugada syndrome; ChIP; channel interacting protein; CPVT; catecholaminergic polymorphic ventricular tachycardia; DCM; dilated cardiomyopathy; EHRA; European Hear
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; AD; autosomal dominant; AR; autosomal recessive; BrS; Brugada syndrome; CPVT; catecholaminergic polymorphic ventricular tachycardia; ECG; electrocardiogram/electrocardiography/electrocardiographic; FDR; first-degree relative; LQTS; long QT syndrome; NGS;
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; CHQ-PF28; Child Health Questionnaire-Parent Form 28; CPVT; catecholaminergic polymorphic ventricular tachycardia; CSDS; Child Sheehan Disability Scale-Parent Form; ICD; implantable cardioverter-defibrillator; LCSD; left cardiac sympathetic denervation
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Long QT syndrome; Catecholaminergic polymorphic ventricular tachycardia; Ion channels; Patch clamp; Arrhythmias;
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; ARVC; arrhythmogenic right ventricular cardiomyopathy/dysplasia; BrS; Brugada syndrome; CI; confidence interval; CPVT; catecholaminergic polymorphic ventricular tachycardia; HCM; hypertrophic cardiomyopathy; ICD; implantable cardioverter-defibrillator; LM
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; 2D12; anti-PLB monoclonal antibody; CaMKII; Ca2Â +/calmodulin-dependent protein kinase; CPVT; catecholaminergic polymorphic ventricular tachycardia; DAD; delay afterdepolarizations; Fab; fab fragment of 2D12; KCa; Ca concentration for half-maximal effect;
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; AP; Action potential; APD; AP duration; BS; Brugada syndrome; CaMKII; Ca-calmodulin kinase II; CPVT; Catecholaminergic polymorphic ventricular tachycardia; CV; Conduction velocity; DAD; Delayed afterdepolarization; EAD; Early afterdepolarization; ERS; Ear
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; ACMG; American College of Medical Genetics; BrS; Brugada syndrome; CPVT; catecholaminergic polymorphic ventricular tachycardia; ECG; electrocardiogram; ICD; implantable cardioverter-defibrillator; LQTS; long QT syndrome; VUS; variants of uncertain/unknown
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; AS; arrhythmia score; cAMP; cyclic adenosine monophosphate; CPVT; catecholaminergic polymorphic ventricular tachycardia; CVA; complex ventricular arrhythmia; ECG; electrocardiogram; EC50; half maximal effective concentration; ETT; exercise treadmill test;
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Channelopathies; Long QT syndrome; Short QT syndrome; Brugada syndrome; Catecholaminergic polymorphic ventricular tachycardia; Sudden cardiac death; ATS; Anderson-Tawil syndrome; AP-A; anthopleurin-A; APD; action potential duration; BrS; Brugada syndrom
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Brugada syndrome; catecholaminergic polymorphic ventricular tachycardia; long QT syndrome; short QT syndrome; sudden cardiac death
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Ion channel; Auxiliary subunit; Cardiac arrhythmia; Catecholaminergic polymorphic ventricular tachycardia; Ankyrin-B syndrome;
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; ARVC; arrhythmogenic right ventricular cardiomyopathy; CASPER; Cardiac Arrest Survivors with Preserved Ejection Fraction Registry; CPVT; catecholaminergic polymorphic ventricular tachycardia; ECG; electrocardiogram/electrocardiographic; ERS; early repolar
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Long-QT syndrome; Short-QT syndrome; Brugada syndrome; Catecholaminergic polymorphic ventricular tachycardia; Ventricular fibrillation;
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; ADL; activity of daily living; ARVC; arrhythmogenic right ventricular cardiomyopathy; CI; confidence interval; CPVT; catecholaminergic polymorphic ventricular tachycardia; ECG; electrocardiogram/electrocardiography; HCM; hypertrophic cardiomyopathy; IQR;
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; AF; atrial fibrillation; AP; action potential; BrS; Brugada syndrome; BWS; Beckwith-Wiedemann syndrome; Ca2Â +; calcium; CCD; cardiac conduction disease; CNV; copy number variation; CPVT; catecholaminergic polymorphic ventricular tachycardia; DCM; dilat
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; 3'UTR; 3' untranslated region; BrS; Brugada syndrome; Ca2+; calcium; CCD; cardiac conduction disturbance; CPVT; catecholaminergic polymorphic ventricular tachycardia; ECG; electrocardiogram; GWAS; genome-wide association study; K+; potassium; LQTS; lo
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; cardiac arrest; catecholaminergic polymorphic ventricular tachycardia; obstetric emergency; pregnancy; simulation-based learning;
Pathogenic mechanism of a catecholaminergic polymorphic ventricular tachycardia causing-mutation in cardiac calcium release channel RyR2
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Cardiac arrhythmias; Catecholaminergic polymorphic ventricular tachycardia; Calcium release channel; Disease-causing mutation; Pathogenic mechanism;
Sorcin ablation plus β-adrenergic stimulation generate an arrhythmogenic substrate in mouse ventricular myocytes
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; AP; action potential; BAPTA; 1,2-bis(o-aminophenoxy)ethane-N,N,Nâ²,Nâ²-tetraacetic acid; BVT; bidirectional ventricular tachycardia; CPVT; catecholaminergic polymorphic ventricular tachycardia; DAD; delayed afterdepolarization; EAD; early afterdepolariz
Accentuated vagal antagonism paradoxically increases ryanodine receptor calcium leak in long-term exercised Calsequestrin2 knockout mice
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Accentuated antagonism; Arrhythmia; Calcium; Catecholaminergic polymorphic ventricular tachycardia; Exercise; Vagal reflex;
Mutation-linked, excessively tight interaction between the calmodulin binding domain and the C-terminal domain of the cardiac ryanodine receptor as a novel cause of catecholaminergic polymorphic ventricular tachycardia
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Arrhythmia; Calmodulin; Catecholaminergic polymorphic ventricular tachycardia; Excitation-contraction coupling; Ryanodine receptor;
Stabilization of Ca2+ signaling in cardiac muscle by stimulation of SERCA
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Cardiac myocytes; Calcium signaling; Sarcoplasmic reticulum calcium pump; Calcium waves; Arrhythmia; AP; Action Potential; β-AR; β-adrenergic receptor; CaMKII; Calmodulin kinase II; CICR; Ca2+-induced Ca2+ release; CPVT; Catecholaminergic polymorphic ve
A novel variant in RyR2 causes familiar catecholaminergic polymorphic ventricular tachycardia
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Sudden cardiac death; Catecholaminergic polymorphic ventricular tachycardia; Genetics; RyR2;
A novel RYR2 loss-of-function mutation (I4855M) is associated with left ventricular non-compaction and atypical catecholaminergic polymorphic ventricular tachycardia
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Ryanodine receptor-2; Catecholaminergic polymorphic ventricular tachycardia; Left ventricular non-compaction; Sudden unexpected death; Arrhythmia;
Beta-blocker therapy for long QT syndrome and catecholaminergic polymorphic ventricular tachycardia: Are all beta-blockers equivalent?
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Beta-blockers; Catecholaminergic polymorphic ventricular tachycardia; Long QT syndrome; Nadolol; Sudden death;
A type 2 ryanodine receptor variant associated with reduced Ca2+ release and short-coupled torsades de pointes ventricular arrhythmia
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Torsades de pointes; Catecholaminergic polymorphic ventricular tachycardia; Idiopathic ventricular fibrillation; RyR2; Long QT;
Suppression of Arrhythmia by Enhancing Mitochondrial Ca2+ Uptake in Catecholaminergic Ventricular Tachycardia Models
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; CPVT; MCU; MiCUp; mitochondria; RyR2; VDAC2; CPVT; catecholaminergic polymorphic ventricular tachycardia; epi/caff; epinephrine/caffeine; iPSC; induced pluripotent stem cell; ISO; isoproterenol; MCU; mitochondrial calcium uniporter; MiCUp; mitochondrial c
Utility of Post-Mortem Genetic Testing in Cases of Sudden Arrhythmic Death Syndrome
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; cardiomyopathy; channelopathy; molecular autopsy; next-generation sequencing; unexplained sudden death; ACM; arrhythmogenic cardiomyopathy; ACMG; American College of Medical Genetics; BrS; Brugada syndrome; CPVT; catecholaminergic polymorphic ventricular
Channelopathies as Causes of Sudden Cardiac Death
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Brugada syndrome; Catecholaminergic polymorphic ventricular tachycardia; Genetic testing; Ion channels; Long QT syndrome; Ryanodine receptor; Left cardiac sympathetic denervation;
Nadolol decreases the incidence and severity of ventricular arrhythmias during exercise stress testing compared with β1-selective β-blockers in patients with catecholaminergic polymorphic ventricular tachycardia
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; CPVT; catecholaminergic polymorphic ventricular tachycardia; ECG; electrocardiogram/electrocardiographic; ICD; implantable cardioverter-defibrillator; NSVT; nonsustained ventricular tachycardia; RyR2; ryanodine receptor 2; SCA; sudden cardiac arrest; VES;
CaMKII-dependent phosphorylation of RyR2 promotes targetable pathological RyR2 conformational shift
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; AIP; autocamtide-2 related inhibitory peptide; Bmax; binding maximum; CaM; calmodulin; CaMKII; calcium/calmodulin-dependent protein kinase II; CaSpF; calcium spark frequency; CPVT; catecholaminergic polymorphic ventricular tachycardia; DAN; dantrolene; F;
Catecholaminergic polymorphic ventricular tachycardia associated with sinus node dysfunction and junctional rhythm: Case report and literature review
Keywords: تاکیکاردی بطنی پلی مورفید Catecholaminergic; Catecholaminergic polymorphic ventricular tachycardia; Sinus node dysfunction; Junctional rhythm;