Keywords: PrP; prion protein; PrPC; normal cellular isoform of PrP; PrPSc; abnormal misfolded isoform of PrP; CJD; Creutzfeldt Jakob disease; sCJD; sporadic CJD; dCJD; dura mater graft-associated CJD; p-dCJD; plaque-type dCJD; np-dCJD; non-plaque-type dCJD; 129M/M;
مقالات ISI (ترجمه نشده)
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Keywords: PrPc; normal cellular isoform of prion protein; PrPres; abnormal isoform of prion protein; Sct; secretin; SctR; secretin receptor; Secretin receptor; Prion; Gender effect; Incubation time; Knockout mouse; N2a cells;
Keywords: Prion; Biological safety level; Protein; Expression; Purification; Refolding; PrPC; major prion protein of higher animals (cellular form); PrPSC; major prion protein of higher animals (scrapie form); SDS-PAGE; sodium dodecyl sulfate polyacrylamide gel ele
Keywords: Aβ; amyloid-β; AD; Alzheimer's disease; Ahx; aminohexanoic linker; EDC; 1-ethyl-3-(3-dimethylaminopropyl)carbodiimide; fAD; familial form of AD; GPI; glycophosphatidylinositol; HBSS; Hank's balanced salt solution; HFIP; hexafluoro-2-propanol; LDH; lacta
Keywords: AA; amino acid; Aβo; oligomeric β-amyloid; Aβ; β-amyloid; AD; Alzheimer's disease; α7nAChR; α7 nicotinic acetylcholine receptor; ALS; amyotrophic lateral sclerosis; APLP1; amyloid beta precursor-like protein 1; APP; amyloid precursor protein; β-A
Keywords: α-syn; α-synuclein; Aβ; β-amyloid; AD; Alzheimer's disease; ADAMs; a disintegrin and metalloproteinases; ALS; amyotrophic lateral sclerosis; BSE; bovine spongiform encephalopathy; CJD; Creutzfeldt-Jakob disease; CNS; central nervous system; CSF; cer
Keywords: PrPC; cellular prion protein; PrPSc; aggregated form of prion protein; NTR; N-terminal region; CTD; C-terminal domain; α2; helix 2; α3; helix 3; CD; circular dichroism; FTIR; Fourier transform infrared; DLS; dynamic light scattering; wt; wild-type; SEC;
Keywords: Polymer nanocomposites; Conducting polymers; Voltammetric sensors; Electrochemical biosensors; DPV; Differential pulse voltammetry; SWV; Square wave voltammetry; LSV; Linear sweep voltammetry; CV; Cyclic voltammetry; AdSDPV; Adsorptive stripping different
Keywords: PrP; prion protein; PrPc; normal cellular PrP; PrPres; protease-resistant abnormal PrP; JH-III; juvenile hormone III; FOH; farnesol; GGOH; geranylgeraniol; Isoprenoid; Prion; Juvenile hormone; Farnesol; Geranylgeraniol; Cholesterol; Prenylation; N2a cell;
Keywords: DAPI; 4â²,6-diamidino-2-phenylindole; Iba-1; ionized calcium binding adaptor molecule-1; IL; interleukin; iNOS; inducible nitric oxide synthase; LPS; lipopolysaccharide; NF-κB; nuclear transcription factor kappa B; NO; nitric oxide; PrPC; prion protein;
Keywords: PrPC; cellular prion protein; PrPSc; scrapie conformer; DRM; detergent resistant membranes; GPI-AP; glycosylphosphatidylinositol-anchored proteins; ERC; endosomal recycling compartment; ERAD; endoplasmic reticulum associated-proteasomal degradation; RML;
Keywords: PrPC; cellular prion protein; PrPSc; scrapie form of prion protein; [Ca2+]i; intracellular calcium; MPs; microparticles; PMPs; platelet-derived microparticles; Thr; thrombin; PrP; prion peptide; Prion; Platelets; Intracellular calcium; Calpain; Microparti
Keywords: Aβ; amyloid-β peptide; AD; Alzheimer's disease; AFM; atomic force microscopy; ALS; amyotrophic lateral sclerosis; dpi; days post injection; HuPrP; human PrPC; HX-MS; hydrogen/deuterium exchange measured using mass spectrometry; LBs; Lewy bodies; PD; Par
Keywords: Variable domain of heavy-chain antibody; Inhibition of protein misfolding and aggregation; Protein misfolding diseases; Amyloidoses; VHH; Nanobody; Ab; antibody; Aβ; amyloid β-peptide; AD; Alzheimer's disease; ANS; anilino naphthalene-sulfonic acid; AP;
Keywords: Dendritic spine; Synaptic plasticity; Neurodegenerative diseases; Psychiatric disorders; Glutamate receptor; Calcium signaling; ADHD; attention deficit hypersensitive disorders; FXS; Fragile X-syndrome; CNS; central nervous system; GABA; gamma amino butyr
Keywords: Abs; antibodies; Akt; cytoplasmic serine-threonine kinase from Ak mouse strain thymoma; Cbl; cobalamin; Cbl-D; Cbl-deficient; CNS; central nervous system; CSF; cerebrospinal fluid; DMSO; dimethyl sulfoxide; Dpl; Doppel; EGF; epidermal growth factor; GFAP;
Keywords: Aβ; amyloid-β; AD; Alzheimer's disease; ALP; autophagy-lysosome pathway; AMPA; α-amino-3-hydroxy-5-methyl-4-isoxazolepropionic acid; ApoER2; apolipoprotein E receptor 2; APP; Aβ precursor protein; BDNF; brain-derived neurotrophic factor; CSF; cere
Keywords: PrPC; cellular prion protein; PrP-KO; PrP knockout; WT; wild-type; Cellular prion protein; PrP; PrP-KO; Behavior; Transgenic mice;
Keywords: H1, H2, H3; helices 1, 2, and 3; β1, β2; beta sheets 1 and 2; CBDPS; CyanurBiotinDiPropionylSuccinimide; PrPC; native (non-infectious) prion protein; PrPβ; β-oligomeric form of the prion protein; BS3; bis(sulfosuccinimidyl) suberate; EDC; 1-ethyl-3-[3
Keywords: AA; ascorbic acid; BSE; Bovine spongiform encephalopathies; B3LYP; Becke 3 parameter Lee Yang Parr; BP86; Becke Perdew86; CD; Circular dichroism; CJD; Creutzfeldt-Jakob disease; CPMD; Car-Parrinello molecular dynamics; DFT; Density functional theory;
Monomeric amyloid-β reduced amyloid-β oligomer-induced synapse damage in neuronal cultures
Keywords: AD; Alzheimer's disease; APP; amyloid precursor protein; Aβ; amyloid-β; PrPC; cellular prion protein; cPLA2; cytoplasmic phospholipase A2; CSP; cysteine-string protein; ELISA; enzyme-linked immunoassay; Fab; fragment antigen-binding; GPI; glycosylphosph
PTK2B/Pyk2 overexpression improves a mouse model of Alzheimer's disease
Keywords: Alzheimer's disease; Mouse model; Non-receptor tyrosine protein kinase; Pyk2; Src; 5XFAD; mice transgenic for human APP and presenilin1 with 5 mutations found in familial Alzheimer's disease; AAV; adeno-associated virus; Aβ; amyloid β; AD; Alzheimer's d
Monoclonal Antibody DL11C8 Identifies ADAM23 as a Component of Lipid Raft Microdomains
Keywords: ADAM23; a disintegrin and metalloprotease protein 23; CNS; central nervous system; conA; concanavalin A-Sepharose; ELISA; enzyme-linked immunosorbent assay; FCS; fetal calf serum; PrPc; cellular prion protein; TNF; tumor necrosis factor; WGA; wheat germ a
Residue-specific mobility changes in soluble oligomers of the prion protein define regions involved in aggregation
Keywords: Prion protein; Protein misfolding; Beta oligomer; Solution NMR; PrPSc; infectious particle of misfolded prion protein; PrP; prion protein; PrPc; cellular prion protein; BSE; bovine spongiform encephalopathy; CWD; chronic wasting disease; CJD; Creutzfeldt
Research reportPrP-C1 fragment in cattle brains reveals features of the transmissible spongiform encephalopathy associated PrPsc
Keywords: TSE; transmissible spongiform encephalopathy; BSE; bovine spongiform encephalopathy; PK; proteinase K; PrP; prion protein; PrPres; protease-resistant prion protein; PrPsc; disease-associated PrP; PrPc; normal cellular PrP; NaPTA; sodium phosphotungstic ac
Identification and Structural Characterization of the Precursor Conformation of the Prion Protein which Directly Initiates Misfolding and Oligomerization
Keywords: PrP; prion protein; PrPC; cellular PrP; PrPSc; scrapie PrP; HDX; hydrogen-deuterium exchange; moPrP; mouse PrP; PUF; partially unfolded form; CTD; C-terminal domain; dm CTD; double mutant variant of the C-terminal domain; wt; wild-type; DLS; dynamic lig
The retention of prion protein in the endoplasmic reticulum prevents N2A cells from proteasome inhibition-induced cytotoxicity
Keywords: PrPC; PrPSc; Endoplasmic reticulum; KDEL ER-retention motif; Prion disease;
The metalloproteinase ADAM10: A useful therapeutic target?
Keywords: APL; Acute Promyelocytic Leukemia; ADAM; A Disintegrin And Metalloproteinase; AP2; Adaptor Protein-2; AD; Alzheimer's Disease; Aβ; Amyloid beta; APP; Amyloid Precursor Protein; ACE; Angiotensin Converting Enzyme; APRIL; A Proliferation-Inducing Ligand; B
HIV/neuroAIDS biomarkers
Keywords: Aβ42-β; amyloid of 42 kiloDaltons; AD; Alzheimer's disease; APP; amyloid precursor protein; ALS; amyotrophic lateral sclerosis; BOLD; blood oxygen level-dependent contrast imaging; cART; combination anti-retroviral therapy; CBF; cerebral blood flow; C
l-Arginine ethylester enhances in vitro amplification of PrPSc in macaques with atypical L-type bovine spongiform encephalopathy and enables presymptomatic detection of PrPSc in the bodily fluids
Keywords: Atypical bovine spongiform encephalopathy; Protein misfolding cyclic amplification; Arginine ethylester; Bodily fluid; Nonhuman primate; PrPSc; Pathogenic form of prion protein; PrPC; cellular prion protein; CJD; Creutzfeldt-Jakob disease; BSE; Bovine s
Soluble prion protein and its N-terminal fragment prevent impairment of synaptic plasticity by Aβ oligomers: Implications for novel therapeutic strategy in Alzheimer's disease
Keywords: PrPC; membrane-anchored cellular prion protein; rPrP; recombinant human prion protein; Aβ; amyloid β; GPI; glycosylphosphatidylinositol; LTP; long-term potentiation; LDH; lactate dehydrogenase; fEPSPs; field evoked postsynaptic potentials; aCSF; artific
Decoding the function of the N-terminal tail of the cellular prion protein to inspire novel therapeutic avenues for neurodegenerative diseases
Keywords: Prion; PrPC; Aβ oligomers; Alzheimer; Neurodegeneration;
Are PrPCs involved in some human myelin diseases? Relating experimental studies to human pathology
Keywords: Abs; antibodies; Akt; cytoplasmic serine-threonine kinase from Ak mouse strain thymoma; AT; anti-TNF-α; Cbl; cobalamin; Cbl-D; Cbl-deficient; CNS; central nervous system; CoA; coenzyme A; CSF; cerebrospinal fluid; EGF; epidermal growth factor; GFAP; gl
H ferritin silencing induces protein misfolding in K562 cells: A Raman analysis
Keywords: 2'-7'-DCF; 2'-7'-dichlorodihydrofluorescein; AβP; β-amiloid protein; BCA; bicinchoninic acid; CM-H2CFDA, 5-(and-6)-carboxy-2'; 7'dichlorofluorescein; DCDR; drop coating deposition Raman; EMSC; extended multiplicative signal correction; FHC; ferr
Protein misfolding cyclic amplification (PMCA): Current status and future directions
Keywords: TSEs; transmissible spongiform encephalopathies; PrPTSE; disease associated misfolded PrP; PrPC; cellular prion protein; PrPres; proteinase K resistant misfolded PrP; PrP27-30; proteinase K resistant core of misfolded PrP; rPrP; recombinant PrP; PMCA; p
Prion protein functions as a ferrireductase partner for ZIP14 and DMT1
Keywords: Dcytb; duodenal cytochrome b; DMT1; divalent metal transporter-1; FAC; ferric ammonium citrate; FR; ferrireductase; GFP; Green-fluorescent protein; ip; intraperitoneal; LIP; labile iron pool; NTBI; non-transferrin-bound iron; PrPC; prion protein; SDS-PAGE
Stabilization of microtubular cytoskeleton protects neurons from toxicity of N-terminal fragment of cytosolic prion protein
Keywords: CtmPrP; transmembrane form of prion protein with the C-terminus residing in the lumen of endoplasmic reticulum; cytoPrP; cytosolic prion protein; ER; endoplasmic reticulum; GPI; glycosylphosphatidylinositol; GSK-3; glycogen synthase kinase 3; HBSS; Hank's
Selective multifaceted E3 ubiquitin ligases barricade extreme defense: Potential therapeutic targets for neurodegeneration and ageing
Keywords: AAD; active adenylation domain; 4-PBA; 4-phenylbutyric acid; 6-OHDA; 6-hydroxydopamine; ABCG5/8; ATP-binding cassette sub-family G member 5/8; AD; Alzheimer's disease; AIB1; amplified in breast cancer 1; AIP4; atrophin-1 interacting protein 4; AMPA; α-
Methionine oxidation accelerates the aggregation and enhances the neurotoxicity of the D178N variant of the human prion protein
Keywords: PrP; prion protein; PrPC; the normal cellular PrP; FFI; fatal familial insomnia; huPrP; human prion protein; HPLC; high performance liquid chromatography; MS; mass spectrometry; MALDI-TOF; matrix-assisted laser desorption/ionization time-of-flight; LC; li
Molecular cloning and sequence analysis of prion protein gene in Xiji donkey in China
Keywords: TSEs; transmissible spongiform encephalopathies; CJD; Creutzfeldt-Jakob disease; vCJD; variant Creutzfeldt-Jakob diseases; BSE; bovine spongiform encephalopathy; CWD; chronic wasting disease; FME; feline spongiform encephalopathy; TME; mink spongiform
Prion formation correlates with activation of translation-regulating protein 4E-BP and neuronal transcription factor Elk1
Keywords: PrPC; normal cellular prion protein; PrPSc; disease-associated prion protein; GT1-1 cells; immortalized hypothalamic gonadotropin-releasing hormone neurons; BDNF; brain-derived neurotrophic factor; MEK; mitogen-activated protein kinase kinase; ERK; extrac
Lysine hydroxylation and O-glycosylation in the globular, C-terminal region of mammalian-expressed, recombinant PrP
Keywords: CAD; collisionally activated dissociation; CHO; Chinese hamster ovary; GPI; glycosylphosphatidylinositol; MS; mass spectrometry; MS/MS; tandem mass spectrometry; PRNP; the gene encoding the prion protein; PrPC; cellular prion protein; PrPSc; scrapie isofo
De novo galectin-3 expression influences the response of melanoma cells to isatin-Schiff base copper (II) complex-induced oxidative stimulus
Keywords: [Cu(isaepy)2](ClO4)2; [bis-(2-oxindol-3-yl-imino)-2-(2-aminoethyl) pyridine-N,N'] copper (II) perchlorate; [Zn(isaepy)Cl2]; [dichloro (2-oxindol-3-yl-imino)-2-(2-aminoethyl) pyridine-N,Nâ²] zinc (II); AMPK; adenosine monophosphate-activated protein kin
PrPC interacts with potassium channel tetramerization domain containing 1 (KCTD1) protein through the PrP51-136 region containing octapeptide repeats
Keywords: TSEs, transmissible spongiform encephalopathies; BSE, bovine spongiform encephalopathy; CJD, Creutzfeldt–Jacob disease; KCTD1, potassium channel tetramerization domain containing 1Prion; PrPC; KCTD1
Persistence of the bovine spongiform encephalopathy infectious agent in sewage
Keywords: BSE; bovine spongiform encephalopathy; CWD; chronic wasting disease; TSE; transmissible spongiform encephalopathies; PrPc; cellular prion protein; PrPSc; scrapie-associated prion protein; PrPRes; protease-resistant prion protein; Prions; BSE; PrPRes; Infe
Copper(II) complexation to 1-octarepeat peptide from a prion protein: Insights from theoretical and experimental UV-visible studies
Keywords: Copper complex; Peptide; DFT; Octarepeat domain; Prion; PrPC
Change in the characteristics of ferritin induces iron imbalance in prion disease affected brains
Keywords: PrPSc; PrP-scrapie; PrPC; normal cellular PrP; Tf; transferrin; Cp; ceruloplasmin; Prions; Ferritin; Iron imbalance; Aggregation; Neurotoxicity;
Hypoxia-inducible factor-1 alpha regulates prion protein expression to protect against neuron cell damage
Keywords: prp106-126; Neuron cell; Hypoxia; HIF-1α; PrPC;
Overexpression of cellular prion protein (PrPC) prevents cognitive dysfunction and apoptotic neuronal cell death induced by amyloid-β (Aβ1-40) administration in mice
Keywords: Aβ; amyloid-β; AD; Alzheimer's disease; ANOVA; analysis of variance; Ca2+; calcium; DMSO; dimethyl sulfoxide; E; east; i.c.v.; intracerebroventricular; i.p.s.p.; inhibitory postsynaptic potentials; K+; potassium; KRB; Krebs-Ringer bicarbonate buffer
Cobalamin (vitamin B12) regulation of PrPC, PrPC-mRNA and copper levels in rat central nervous system
Keywords: Abs; antibodies; ANOVA; analysis of variance; AT; anti-TNF-α; C; cervical; Cbl; cobalamin; Cbl-D; Cbl-deficient; CNS; central nervous system; CSF; cerebrospinal fluid; Ct; cycle threshold; H; the 6H4 region of the normal prion molecule; ECL; enhanced che