Keywords: CPR; cardiopulmonary resuscitation; CMC; complex medical conditions; CRF; chronic respiratory failure; EMS; Emergency Medical Services; LTMV; long term mechanical ventilation; VCP; ventilator care program; Interprofessional care team; Long-term mechanical
مقالات ISI (ترجمه نشده)
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Keywords: FK228 (PubChem CID: 5352062); PXD101 (PubChem CID: 6918638); SAHA (PubChem CID: 5311); LBH-589 (PubChem CID: 6918837); tubacin (PubChem CID: 6675804); tubastatin A (PubChem CID: 49850262); ACY-1215 (PubChem CID: 53340666); ACY-241 (PubChem CID: 53340426);
Keywords: Inclusion Body Myopathy; Paget disease; IBMPFD; VCP; IBMFRS; Dynamometry;
Keywords: VCP; p97; Inclusion body myopathy; Paget's disease of bone; Parkinson's disease; Novel VCP mutations;
Keywords: 3-MC; 3-methylcholanthrene; Ah; aryl hydrocarbon; AhE; aryl hydrocarbon receptor; AP-1; activator protein-1; ARE; antioxidant response element; ATF4; activating transcription factor 4; β-NF; β-naphthoflavone; β-NF-RE; β-NF-responsive element; β-TRCP;
Keywords: DES; direct electrical stimulation; CCEP; cortico-cortical evoked potential; SPES; single pulse electrical stimulation; ALA; anterior language area; PLA; posterior language area; VCP; volume-conducted potential; PCA; principal component analysis; ECoG; el
Keywords: p97; Valosin-containing protein; VCP; Eeyarestatin I; EerI; Solubility;
Keywords: AMA; amantadine; BFM; bond fluctuation method; BST-2; bone marrow stromal cell antigen 2; CD; circular dichroism; CGMD; coarse-grained molecular dynamics; ClyA; cytolysin A; DHPC; dihexanoylphosphocholine; DPC; dodecylphosphocholine; E. coli; Escherichia
Keywords: Cell migration; Autophagy; Filopodia; Lamellipodia; Target identification; 14-3-3; GLUT; VCP;
Keywords: HIBM; hereditary inclusion-body myopathy; s-IBM; sporadic inclusion-body myositis; GNE; UDP-N-acetylglucosamine 2-epimerase/N-acetylmannosamine kinase; GNE/MNK; UDP-GlcNAc 2-epimerase/ManNAc kinase; DMRV; distal myopathy with rimmed vacuoles; CK; creatine
Keywords: Inclusion body myositis; VCP; Hereditary inclusion body myopathy; Myofibrillar myopathy; Amyotrophic lateral sclerosis;
Keywords: ASK1; apoptosis signal-regulating kinase; ALS; amyotrophic lateral sclerosis; Apaf-1; apoptotic protease-activating factor; ATF6; activating transcription factor 6; Atg12; autophagy-related gene 12; C9ORF72; chromosome 9 open reading frame 72; CHIP; carbo
Keywords: Proteome; Pubertal mice; Testis; Carbon ion radiation; HIR; heavy ions radiation; 2-DE; two-dimensional gel electrophoresis; MALDI-TOF-TOF; matrix-assisted laser desorption/ionization tandem time-of-flight mass spectrometry; HIRFL; heavy ion research faci
Keywords: ALS; SOD1; TARDBP; FUS; OPTN; VCP; UBQLN2; SQSTM1; PFN1; HNRNPA1; ATXN2; C9ORF72;
Keywords: AID; activation-induced cytidine deaminase; H. pylori; Helicobacter pylori; IARC; International Agency for Research on Cancer; GI; gastrointestinal; CI; confidence interval; KLF5; Krüppel-like factor 5; VCP; valosin-containing protein; OLGA; Operative Li
The heterozygous R155C VCP mutation: Toxic in humans! Harmless in mice?
Keywords: VCP; p97; R155C VCP knock-in mice; IBMPFD; ALS; Multisystem proteinopathy;
Molecular epidemiological study of familial amyotrophic lateral sclerosis in Japanese population by whole-exome sequencing and identification of novel HNRNPA1 mutation
Keywords: Familial amyotrophic lateral sclerosis; HNRNPA1; TBK1; VCP; Whole-exome sequencing analysis; Stress granule;
Depletion of Ubiquilin induces an augmentation in soluble ubiquitinated Drosophila TDP-43 to drive neurotoxicity in the fly
Keywords: Ubiquilin; Altered proteostasis; TDP-43 pathology; Drosophila; VCP; ALS-FTD;
Hippo, Drosophila MST, is a novel modifier of motor neuron degeneration induced by knockdown of Caz, Drosophila FUS
Keywords: ALS; amyotrophic lateral sclerosis; Caz; Cabeza; CNS; central nervous system; DAPI; 4,6-diamino-2-phenylidole dihydrochloride; FALS; familial amyotrophic lateral sclerosis; FUS; Fused in Sarcoma; hpo; Hippo; HRP; horseradish peroxidase; MST; Mammalian ste
Nacre-inspired composite design approaches for large-scale cementitious members and structures
Keywords: Bio-inspired; Cementitious composites; Energy dissipation; Mesh reinforcement; Fiber reinforced; Strain-hardening cementitious composites; SHCCs; Strain-hardening cementitious composites, also called Engineered Cementitious Composites (ECCs), or “bendab
Exploring the multifaceted roles of heat shock protein B8 (HSPB8) in diseases
Keywords: Aβ; amyloid β-peptide; ACD; α-crystallin domain; AD; Alzheimer disease; ALS; amyotrophic lateral sclerosis; AR; androgen receptor; BAG3; BCL2 associated athanogene 3; BMP; bone morphogenetic protein; CASA; chaperone-assisted selective autophagy; CHIP;
Genetic analysis of VCP and WASH complex genes in a German cohort of sporadic ALS-FTD patients
Keywords: Amyotrophic lateral sclerosis; Frontotemporal lobar degeneration; FTLD-ALS; VCP; Strumpellin; CAPZ; CCDC53; WASH complex;
Assessment of ocular discomfort caused by 5 shampoos using the Slug Mucosal Irritation test
Keywords: VCP; veterinary care products; SLES; sodium laureth sulfate; Slug Mucosal Irritation test; Ocular discomfort; Veterinary shampoos;
Identification of potential target genes and related regulatory transcription factors in spontaneous hairline fracture induced by hypervitaminosis A
Keywords: DGEs; differentially expressed genes; GEO; Gene Expression Omnibus; BH; Benjamini and Hochberg; Derl1; derlin 1; VCP; valosin-containing protein; Sec24c; SEC24 homolog C; COPII; coat complex component; Uba1; ubiquitin-like modifier activating enzyme 1; Ub
New genes for accurate normalization of qRT-PCR results in study of iPS and iPS-derived cells
Keywords: ACTb; actin beta; AFS; amniotic fluid stem cells; B2M; beta-2-microglobulin; bFGF; basic fibroblast growth factor; C1orf43; chromosome 1 open reading frame 43; CHMP2A; charged multivesicular body protein 2A; EMC7; ER membrane protein complex subunit 7; ES
Seguimiento a 30 dÃas tras el implante percutáneo de válvula aórtica CoreValve Evolut R: estudio prospectivo de pacientes no seleccionados
Keywords: Implante percutáneo de válvula aórtica; Estenosis valvular aórtica; Válvula autoexpandible; Fuga paravalvular; Implante de marcapasos; Evolut R; Transcatheter aortic valve implantation; Aortic valve stenosis; Self-expanding valve; Paravalvular leak;
Roles for the VCP co-factors Npl4 and Ufd1 in neuronal function in Drosophila melanogaster
Keywords: Proteasome; TDP-43 accumulation; Neurodegeneration; Drosophila; ALS; amyotrophic lateral sclerosis; IBMPDF; inclusion body myopathy with Paget's disease of the bone and frontotemporal dementia; NMJ; neuromuscular junction; Npl4; nuclear protein localizati
Análisis informatizado del ritmo cardÃaco fetal durante la gestación
Keywords: Ritmo cardÃaco fetal; RCF; Análisis informatizado; Variabilidad a corto plazo; VCP; Gestación de riesgo; Vigilancia fetal;
Tratamientos percutáneos de la valvulopatÃa tricuspÃdea: una nueva esperanza para la válvula «olvidada»
Keywords: ValvulopatÃa tricuspÃdea; Transcatéter; Percutáneo; Insuficiencia tricuspÃdea; Tricuspid valve disease; Transcatheter; Percutaneous; Tricuspid regurgitation; ACD; arteria coronaria derecha; ETE 3D; ecocardiografÃa transesofágica tridimensional; IT;
HSPA5 Gene encoding Hsp70 chaperone BiP in the endoplasmic reticulum
Keywords: aa; amino acid; ATF6; activating transcription factor 6; BIK; BCL2-interacting killer; BiP; binding immunoglobulin protein; CD86; cluster of differentiation 86; CHOP; CCAAT-enhancer-binding protein homologous protein; Derlin-1; degradation in ER protein 1
Valosin-containing protein (VCP) is a novel IQ motif-containing GTPase activating protein 1 (IQGAP1)-interacting protein
Keywords: IQGAP1; VCP; Proteomics;
Structure and functions of the chaperone-like p97/CDC48 in plants
Keywords: ADIN; antibody-dependent intracellular neutralization; ARF; ADP ribosylation factor; AAAÂ + ATPase; ATPase associated with diverse cellular activities; CDC48; cell division cycle 48; CAD; chromatin associated degradation; ER; endoplasmic reticulum; ERAD;
Valosin-containing protein (VCP/p97) plays a role in the replication of West Nile virus
Keywords: VCP; WNV replication; Early steps; Genome replication;
One family, one gene and three phenotypes: A novel VCP (valosin-containing protein) mutation associated with myopathy with rimmed vacuoles, amyotrophic lateral sclerosis and frontotemporal dementia
Keywords: Inclusion body myopathy; Frontotemporal dementia; Amyotrophic lateral sclerosis; VCP; Valosin-containing protein
Rare variants in SQSTM1 and VCP genes and risk of sporadic inclusion body myositis
Keywords: Sporadic inclusion body myositis; sIBM; SQSTM1; VCP; Genetic risk factor;
Acoustic resonances in a 3D open cavity with non-parallel walls
Keywords: ed; edge diffraction; ed-spr; edge diffraction specularly; FEM; Finite Element Method; FRF; Frequency Response Function; IS; Image Source; ISM; Image Source Model; LA; Limit Anticlockwise; LC; Limit Clockwise; PML; Perfectly Matching Layer; PO; Polygon Or
VCP/Cdc48 rescues the growth defect of a GPI10 mutant in yeast
Keywords: Cdc48; Endoplasmic reticulum; Gpi10; VCP; Temperature-sensitivity; GPI-anchor;
Cryo-EM of the pathogenic VCP variant R155P reveals long-range conformational changes in the D2 ATPase ring
Keywords: VCP; ATPase; VCP cofactors interaction; Cryo-EM; Mutations and disease;
The NVL gene confers risk for both major depressive disorder and schizophrenia in the Han Chinese population
Keywords: NVL; nuclear VCP/p97-Like; GWAS; the genome-wide association study; MDD; major depressive disorder; SCZ; schizophrenia; LD; linkage disequilibrium; OR; odds ratio; AAA-ATPase; ATPases associated with various cellular activities; hTERT; human telomerase re
Differential recruitment of UBQLN2 to nuclear inclusions in the polyglutamine diseases HD and SCA3
Keywords: polyQ; polyglutamine; HD; Huntington's disease; HTT; Huntingtin protein; SCA3; spinocerebellar ataxia type 3; UPP; ubiquitin-proteasome pathway; UBL; ubiquitin-like domain; UBA; ubiquitin-associated domain; PLIC-1; integrin-associated protein and cytosk
Autophagy receptor defects and ALS-FTLD
Keywords: ALS; FTLD; SQSTM1/p62; Optineurin; VCP; Ubiquilin; Autophagy; Stress granules;
Molecular basis of chromatic adaptation in pennate diatom Phaeodactylum tricornutum
Keywords: CLH; Chromera light harvesting; DL; day light; DM; n-dodecyl β-d-maltoside; F; fluorescence; DCMU; 3-(3,4-dichlorophenyl)-1,1-dimethylurea; FCP; fucoxanthin-chlorophyll protein; Chl(s); chlorophyll(s); LL; low light; MS; mass spectrometry; PCP; peridinin
Proteomic profile of the skin mucus of farmed gilthead seabream (Sparus aurata)
Keywords: Apo-A1; apolipoprotein-A1; ENOA; enolase; FABP7; brain-type fatty acid binding protein; FBPA; fructose-bisphosphate aldolase; GAPDH; glyceraldehyde-3-phosphate dehydrogenase; HSC70; heat-shock cognate 70Â kDa protein; HBB; beta globin; LPS; lipopolysaccha
Should I stay or should I go: VCP/p97-mediated chromatin extraction in the DNA damage response
Keywords: CPDs; Cyclobutane pyrimidine dimers; DSBs; DNA double-strand breaks; ER; endoplasmic reticulum; ERAD; ER-associated degradation; HR; homologous recombination; 6-4PPs; pyrimidine-pyrimidone [6-4] photoproducts; IR; ionizing radiation; UBD; ubiquitin-bindin
Opportunities for translation: Targeting DNA repair pathways in pancreatic cancer
Keywords: ATR; ATM-Rad3-related; BER; base excision repair; Chk1; checkpoint kinase 1; DDR; DNA damage response and repair; DNA-PKcs; DNA-PK catalytic subunit; DOT1L; DOT1-like; DSB; double strand break; FOLFIRINOX; folinic acid, 5-FU, irinotecan, oxaliplatin; 5-FU
Create and preserve: Proteostasis in development and aging is governed by Cdc48/p97/VCP
Keywords: AAA; ATPase associated with diverse cellular activities; AD; Alzheimer's disease; ALS; amyotrophic lateral sclerosis; AMPK; adenosine monophosphate activated kinase; Cdc48/CDC-48; cell division cycle protein 48; DUB; de-ubiquitylating enzyme; ERAD; endopl
SQSTM1 mutations - Bridging Paget disease of bone and ALS/FTLD
Keywords: ALS; amyotrophic lateral sclerosis; aPKC; atypical protein kinase C; C9orf72; chromosome 9 open reading frame 72; FTD; frontotemporal dementia; FTLD; frontotemporal lobar degeneration; FUS/TLS; fused in sarcoma/translocated in liposarcoma; GWAS; genome-wi
Photoprotective sites in the violaxanthin-chlorophyll a binding Protein (VCP) from Nannochloropsis gaditana
Keywords: VCP; violaxanthin-chlorophyll a binding protein; Car; carotenoid; Chl; chlorophyll; LHC; light harvesting complex; FCP; fucoxanthin chlorophyll a/c binding protein; LHC-II; light harvesting complex of Photosystem II; ZFS; zero-field splitting; TR-EPR; T
Frontotemporal lobar degeneration: Diversity of FTLD lesions
Keywords: Frontotemporal lobar degeneration; Frontotemporal dementia; Tau; FUS; TDP-43; Pick's disease; Progranulin; C9ORF72; VCP; Multisystem proteinopathy; NIFID; BIBD; Dégénérescence lobaire frontotemporale; Démence frontotemporale; Tau; FUS; TDP-43; Maladie
Ataxin-3 protein modification as a treatment strategy for spinocerebellar ataxia type 3: Removal of the CAG containing exon
Keywords: SCA3; spinocerebellar ataxia type 3; MJD; Machado-Joseph disease; PolyQ; polyglutamine; ATXN3; ataxin-3; UIMs; ubiquitin interacting motifs; RNAi; RNA interference; AON; antisense oligonucleotide; SNP; single nucleotide polymorphism; DMD; Duchenne muscu