
In vivo evidence of mitochondrial dysfunction and altered redox homeostasis in a genetic mouse model of propionic acidemia: Implications for the pathophysiology of this disorder
Keywords: βF1; ATP synthase, F1 complex, beta polypeptide; BNP; brain natriuretic peptide; C-III; complex III; COX-II; cytochrome c oxidase subunit II; COX-IV; cytochrome c oxidase subunit IV; DAPI; 4â²,6-diamidino-2-phenylindole; DHE; dihydroethidium; GPx1; glut