Keywords: ALS; Amyotrophic lateral sclerosis; DMD; DuchenneMuscular Dystrophy; SMA; Spinalmuscular atrophy; FAP; FamilialAmyloid Polyneuropathy; OD; Orphandisease; ORD; Officeof Rare Diseases; NIH; NationalInstitutes of Health; sALS; SporadicALS; fALS; FamilialALS;
مقالات ISI (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: ATPS; aqueous two phase system; PEO; polyethylene oxide; Pu; pullulan; SALS; small angle light scattering; Montmorillonite; Emulsion; Water-in-water; Pullulan; Polyethylene oxide; ATPS;
Keywords: Familial ALS; Association studies; Genes; Sporadic ALS; ALS; Genetic; SALS; fALS;
Keywords: ALS; Amyotrophic lateral sclerosis; Bcl; 2 B-cell lymphoma-2; COX-2; cyclooxygenase-2; DHYZ; DihuangYinziFang; DPPH; 2,2-diphenyl-1-picrylhydrazyl; FALS; familial Amyotrophic lateral sclerosis; FasL; Fas ligand; FDA; Food and Drug Administration; IFN; Int
Keywords: ABIN; A20 binding and inhibitor of NF-κB; AD; Alzheimer's disease; ALS; amyotrophic lateral sclerosis; Atg; autophagy-related gene; C9ORF72; chromosome 9 open reading frame 72; CC; coiled-coil; cIAP; cellular inhibitor of apoptosis protein; CYLD; cylin
Keywords: CD39; M1/M2 microglia; Motoneuron; Oligodendrocyte; P2X7; P2Y12; ALS; amyotrophic lateral sclerosis; BBG; Brilliant Blue G; BDNF; brain-derived neurotrophic factor; BzATP; 2â²-3â²-O-(benzoyl-benzoyl) ATP; fALS; familial ALS; FUS; fused in sarcoma; HuR
Keywords: Amyotrophic lateral sclerosis; Spinal motor neuron degeneration; Inhibitory circuits; GABA; Glycine; Acetylcholine; Renshaw cell; ALS; amyotrophic lateral sclerosis; SOD1; superoxide dismutase type 1; FALS; familial amyotrophic lateral sclerosis; SALS; sp
Keywords: SALS; SMA; SMN1; SMN2; Veldink formula
Hippo, Drosophila MST, is a novel modifier of motor neuron degeneration induced by knockdown of Caz, Drosophila FUS
Keywords: ALS; amyotrophic lateral sclerosis; Caz; Cabeza; CNS; central nervous system; DAPI; 4,6-diamino-2-phenylidole dihydrochloride; FALS; familial amyotrophic lateral sclerosis; FUS; Fused in Sarcoma; hpo; Hippo; HRP; horseradish peroxidase; MST; Mammalian ste
Astrocyte elevated gene-1 is a novel regulator of astrogliosis and excitatory amino acid transporter-2 via interplaying with nuclear factor-κB signaling in astrocytes from amyotrophic lateral sclerosis mouse model with hSOD1G93A mutation
Keywords: ALS; Amyotrophic lateral sclerosis; AEG-1; Astrocyte elevated gene-1; ACM; astrocyte-conditioned medium; CBP; CREB-binding protein; COX-2; Cyclooxygenase-2; DMSO; dimethyl sulfoxide; DL-NBP; DL-3-n-butylphthalide; DMEM; Dulbecco modified Eagle medium; EAA
CHI3L1 and CHI3L2 overexpression in motor cortex and spinal cord of sALS patients
Keywords: ALS; amyotrophic lateral sclerosis; sALS; sporadic ALS; FALS; familial ALS; CNS; central nervous system; CHI3L1; chitinase 3 like 1; CHI3L2; chitinase 3 like 2; CLPs; chitinase-like proteins; SIVE; Simian Immunodeficiency Virus Encephalitis; TDP-43; TAR D
The relevance of contact-independent cell-to-cell transfer of TDP-43 and SOD1 in amyotrophic lateral sclerosis
Keywords: ALS; amyotrophic lateral sclerosis; CFTR; cystic fibrosis transmembrane conductance regulator; CNS; central nervous system; CSF; cerebrospinal fluid; fALS; familial ALS; FTLD; frontotemporal lobar degeneration; LMN; lower motor neurons; sALS; sporadic ALS
ALS-FTLD associated mutations of SQSTM1 impact on Keap1-Nrf2 signalling
Keywords: ALS; Amyotrophic lateral sclerosis; ARE; Antioxidant response element; FTLD; Frontotemporal lobar degeneration; IKKβ; Inhibitor of nuclear factor kappa-B kinase subunit beta; Keap1; Kelch-like ECH-associated protein 1; KIR; Keap1-interacting region; LIR;
Characterization and comparison of ATF and TFF in stirred bioreactors for continuous mammalian cell culture processes
Keywords: 2-AB; 2-aminobenzamide; AMM; ammonia; ATF; alternating tangential flow; CCC; critical coagulation concentration; GLC; glucose; HF; hollow fiber; LAC; lactate; LMH; cross flow rate per unit area and volume; PES; polyether sulfone; PMMA; poly(methyl methacr
Expression of microRNAs in human post-mortem amyotrophic lateral sclerosis spinal cords provides insight into disease mechanisms
Keywords: AD; Alzheimer's disease; ALS; amyotrophic lateral sclerosis; AQP1; aquaporin 1; BCDIN3D; BCDIN3 domain-containing methyltransferase; BioGRID; Biological Genomic Repository for Interaction Datasets; C9ORF72; chromosome 9 open reading frame 72; CCL2; chemok
TDP-43/FUS in motor neuron disease: Complexity and challenges
Keywords: AD; Alzheimer's disease; Ago2; Argonaute 2; ALS; Amyotrophic lateral sclerosis; ALS/PD; amyotrophic lateral sclerosis and Parkinsonism-dementia complex; AMPA; α-amino-3-hydroxy-5-methyl-4-isoxazolepropionic acid; ATF3; activating transcription factor 3
SMN1 duplications contribute to sporadic amyotrophic lateral sclerosis susceptibility: Evidence from a meta-analysis
Keywords: SMN1 deletions; SMN1 duplications; SMN2 homozygous deletions; Copy number variants; SALS; Meta-analysis; Susceptibility;
ReviewFocality, stochasticity and neuroanatomic propagation in ALS pathogenesis
Keywords: ALS; amyotrophic lateral sclerosis; FALS; familial ALS; FTD; frontotemporal dementia; LMN; lower motor neuron; PLS; primary lateral sclerosis; PMA; progressive muscular atrophy; SALS; sporadic ALS; UMN; upper motor neuron; ALS; PLS; PMA; Motor neuron dise
Altered miRNA expression is associated with neuronal fate in G93A-SOD1 ependymal stem progenitor cells
Keywords: ALS; amyotrophic lateral sclerosis; Ccnd2; cyclin D2; Dlx2; distal-less homeobox 2; epSPCs; ependymal stem/progenitor cells; FALS; familial ALS; GAD 67; glutamic acid decarboxylase 67; GFAP; glial fibrillary acidic protein; Hes1; hairy and enhancer of spl
Proteomic analysis of FUS interacting proteins provides insights into FUS function and its role in ALS
Keywords: ALS; amyotrophic lateral sclerosis; fALS; familial ALS; sALS; sporadic ALS; 293T; human embryonic kidney (HEK293T) cells; FUS/TLS; Fused in Sarcoma/Translocated in Liposarcoma; GST; glutathione S-transferase; RIPA; radioimmunoprecipitation assay buffer; S
A miRNA signature in leukocytes from sporadic amyotrophic lateral sclerosis
Keywords: miRNA; microRNA; ALS; Amyotrophic lateral sclerosis; sALS; Sporadic Amyotrophic lateral sclerosis; rRNA; Ribosomal ribonucleic acid; mRNA; messenger ribonucleic acid; SLC1A2; solute carrier family 1 member 2; microRNAs; sALS; Leukocytes; Microarray;
ALS patients with mutations in the SOD1 gene have an unique metabolomic profile in the cerebrospinal fluid compared with ALS patients without mutations
Keywords: ALS; amyotrophic lateral sclerosis; FTD; fronto-temporal dementia; NPH; normal pressure hydrocephalus; PBP; progressive bulbar palsy; SBMA; spinobulbar muscular atrophy; SALS; sporadic ALS; FALS; familial ALS; wt; wild-type SOD1 genotype; ALSFRS; ALS Funt
Mitochondrial dysfunction in ALS
Keywords: AEOL-10150; manganese [III] tetrakis[N-Nâ²-diethylimidazolium-2-yl]porphyrin; AMPA; α-amino-3-hydroxy-5-methyl-4-isoxazole propinate; ALS; amyotrophic lateral sclerosis; CCS; copper chaperone for superoxide dismutase; DMPO; 3,4-dihydro-2,3-dimethyl-2H-p
Lactate dyscrasia: a novel explanation for amyotrophic lateral sclerosis
Keywords: Amyotrophic lateral sclerosis; Lou Gehrig's disease; LDH; Aspartate; Malate; Pyruvate; Oxaloacetate; Glutamate; Lactate; ATP; FALS; SALS; Neuronal degeneration; Motoneuron; Neuromuscular junction; Lactate shuttle; Mitochondria; Respiratory chain; Muscular
Alteration of protein folding and degradation in motor neuron diseases: Implications and protective functions of small heat shock proteins
Keywords: ALS; amyotrophic lateral sclerosis; AR; androgen receptor; ATG5; autophagy-related gene 5; Bag; Bcl-2 associated athanogene; CBP; CREB-binding protein; CMA; chaperone-mediated autophagy; CMT; Charcot-Marie-Tooth; DAO; d-amino acid oxidase; DCTN1; dynactin
Dysfunction of constitutive and inducible ubiquitin-proteasome system in amyotrophic lateral sclerosis: Implication for protein aggregation and immune response
Keywords: AD; Alzheimer's disease; ALS; amyotrophic lateral sclerosis; ARE; anti-oxidant responsive element; CHIP; carboxyl terminus of Hsc-70 interacting protein; cys; cysteine; CNS; central nervous system; DUB; deubiquitinating enzyme; D3T; dithiole-3-thione; EAE
Identification of a novel D109Y mutation in Cu/Zn superoxide dismutase (sod1) gene associated with amyotrophic lateral sclerosis
Keywords: Superoxide dismutase; Amyotrophic lateral sclerosis; SALS
Mutational analysis of the Cu/Zn superoxide dismutase gene in a Catalan ALS population: Should all sporadic ALS cases also be screened for SOD1?
Keywords: ALS; Familial amyotrophic lateral sclerosis; FALS; SALS; Epidemiology; SOD1; Catalonia; G37R; D76V; D90A; S105L; I112M; N139H; A140A
Guidance of engineered tissue collagen orientation by large-scale scaffold microstructures
Keywords: Tissue engineering; Scaffold; Collagen orientation; SALS; Heart valve
Genetics of familial and sporadic amyotrophic lateral sclerosis
Keywords: Amyotrophic lateral sclerosis; Genetic; FALS; SALS
Proteomic analysis of 4-hydroxy-2-nonenal-modified proteins in G93A-SOD1 transgenic mice-A model of familial amyotrophic lateral sclerosis
Keywords: ALS; amyotrophic lateral sclerosis; sALS; sporadic ALS; fALS; ALS as a familial disorder; mSOD1; mutant SOD1; HNE; 4-hydroxy-2-nonenal; DRP-2; dihydropyrimidinase-related protein 2; Hsp70; heat-shock protein 70; PMSF; phenylmethylsulfonyl fluoride; TCA; t