
Tissue- and species-specific differences in cytochrome c oxidase assembly induced by SURF1 defects
Keywords: سیتوکروم سی اکسیداز; COX; Cytochrome c oxidase; OXPHOS; oxidative phosphorylation system; IMM; inner mitochondrial membrane; RC; respiratory chain; cI-cV; RC complexes I-V; CL; cardiolipin; SCs; respiratory supercomplexes; LS; Leigh syndrome; mtDNA; mitochondrial DNA; DOX