Keywords: گوسفند اپیدرمولیز; Epidermolysis bullosa; Platelet gel; Umbilical cord blood;
مقالات ISI گوسفند اپیدرمولیز (ترجمه نشده)
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در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: گوسفند اپیدرمولیز; Epidermolysis bullosa; autoimmune blistering disease; quality of life; self-esteem;
Keywords: گوسفند اپیدرمولیز; EB; Sleep quality; Sleep disturbances; Epidermolysis bullosa; Anxiety; Depression;
Keywords: گوسفند اپیدرمولیز; bFGF; basic fibroblast growth factor; BJ-iPSC; BJ fibroblast-derived induced pluripotent stem cell; CRISPR/Cas9; clustered regularly interspaced palindromic repeats/CRISPR-associated; DAPI; 4â²,6-diamidino-2-phenylindole; EB; epidermolysis bullosa; EBKC-
Keywords: گوسفند اپیدرمولیز; AT-1; angiotensin II type 1; AT-2; angiotensin II type 2; BM; basement membrane; C/EBP3β; CCAAT/enhancer binding protein β; cSCC; cutaneous squamous cell carcinoma; EB; epidermolysis bullosa; ECM; extracellular matrix; DEB; dystrophic epidermolysis bull
Keywords: گوسفند اپیدرمولیز; Genodermatosis; Epidermolysis bullosa; Epidermolysis bullosa simplex; Epidermolysis bullosa junctional; Epidermolysis bullosa dystrophic; Kindler syndrome; Genetic diagnosis; Antigen mapping; Prenatal diagnosis; Preimplantation diagnosis; Genodermatosis;
Keywords: گوسفند اپیدرمولیز; EB; epidermolysis bullosa; BMZ; basement membrane zone; EBS; epidermolysis bullosa simplex; JEB; junctional epidermolysis bullosa; DEB; dystrophic epidermolysis bullosa; KS; kindler syndrome; DEJ; dermal-epidermal junction; PTC; premature termination codo
Keywords: گوسفند اپیدرمولیز; diacerein; epidermolysis bullosa; keratin; rare genodermatosis; AE; adverse event; BSA; body surface area; CI; confidence interval; EBS; epidermolysis bullosa simplex; EBS-gen/sev; generalized severe epidermolysis bullosa simplex; IFN; intermediate filame
Keywords: گوسفند اپیدرمولیز; EB; epidermolysis bullosa; EBS; EB simplex; JEB; junctional EB; DEB; dystrophic EB; HD; hemidesmosome; LM-332; laminin-332; PTC; premature termination codon; ECM; extracellular matrix; Epidermolysis bullosa; Heritable blistering diseases; Basement membran
Keywords: گوسفند اپیدرمولیز; Epidermolysis Bullosa; Pregnancy; Delivery; Childbirth; Anesthesia;
Keywords: گوسفند اپیدرمولیز; BM; bone marrow; BMSC; bone marrow stem cells; BSA; body surface area; CTACK; cutaneous T cell-attracting chemokine; DDEB; dominant dystrophic epidermolysis bullosa; DEJ; dermo-epidermal junction; EB; epidermolysis bullosa; EBK; epidermolysis bullosa kera
Keywords: گوسفند اپیدرمولیز; EB; epidermolysis bullosa; EBS; epidermolysis bullosa simplex; JEB; junctional epidermolysis bullosa; DEB; dystrophic epidermolysis bullosa;
Keywords: گوسفند اپیدرمولیز; Epidermolysis bullosa; Regional anaesthesia; Caesarean delivery;
Keywords: گوسفند اپیدرمولیز; Epidermolysis bullosa; blisters; pediatrics;
Keywords: گوسفند اپیدرمولیز; DDEB; dominant dystrophic epidermolysis bullosa; EB; epidermolysis bullosa; EBS; epidermolysis bullosa simplex; JEB; junctional epidermolysis bullosa; MGD; meibomian gland dysfunction; RDEB; recessive dystrophic epidermolysis bullosa;
Keywords: گوسفند اپیدرمولیز; Epidermolysis bullosa; Bullous disease; Anemia; Prevalence; Epidemiology; Retrospective study
Keywords: گوسفند اپیدرمولیز; Epidermolysis Bullosa; Pregnancy; Delivery; Childbirth; Anesthesia
Keywords: گوسفند اپیدرمولیز; Syndactyly; Polydactyly; Thumb duplication; Radial longitudinal deficiency; Radial club hand; Thumb hypoplasia; Pollicization; Epidermolysis bullosa;
Keywords: گوسفند اپیدرمولیز; Pyloric atresia; Gastric outlet obstruction; Epidermolysis bullosa
Keywords: گوسفند اپیدرمولیز; Pyloric atresia; Epidermolysis bullosa; Aplasia cutis congenita; Hereditary multiple intestinal atresia;
Keywords: گوسفند اپیدرمولیز; Epidermolysis bullosa; CO2 laser; Commissure stenosis; Minimally invasive laryngo-microsurgery; Arytenoid abduction lateropexy; Pediatric airway stenosis;
A Nonlethal Case of Junctional Epidermolysis Bullosa and Congenital Pyloric Atresia: Compound Heterozygosity in a Patient with a Novel Integrin Beta 4 Gene Mutation
Keywords: گوسفند اپیدرمولیز; junctional epidermolysis bullosa; pyloric atresia; pyloroplasty; surgery; ITGB4 gene mutation; EB; Epidermolysis bullosa; IGB4; Integrin beta 4 gene; JEB; Junctional EB; PA; Pyloric atresia;
Activation of PKB/Akt and p44/42 by mechanical stretch utilizes desmosomal structures and the keratin filament
Keywords: گوسفند اپیدرمولیز; Mechanics; Keratin; Desmosomes; Epidermolysis bullosa;
Research Techniques Made Simple: Genome-Wide Homozygosity/Autozygosity Mapping Is a Powerful Tool for Identifying Candidate Genes in Autosomal Recessive Genetic Diseases
Keywords: گوسفند اپیدرمولیز; AR; autosomal recessive; EB; epidermolysis bullosa; GATK; Genome Analysis Toolkit; HM; homozygosity mapping; Mb; mega base pair; NGS; next-generation sequencing; ROH; region of homozygosity; SNP; single nucleotide polymorphism; WES; whole-exome sequencing
Collagen VII deficient mice show morphologic and histologic corneal changes that phenotypically mimic human dystrophic epidermolysis bullosa of the eye
Keywords: گوسفند اپیدرمولیز; Collagen VII; Epidermolysis bullosa; DEB; RDEB; Cornea; Eye; Scarring; Opacity; Vision loss; Blindness; Mouse; Murine;
The development of induced pluripotent stem cell-derived mesenchymal stem/stromal cells from normal human and RDEB epidermal keratinocytes
Keywords: گوسفند اپیدرمولیز; α-MEM; alpha minimum essential medium; bFGF; basic fibroblast growth factor; BIO; 6-bromoindirubin-3â²-oxime; BM-MSCs; bone marrow-derived MSCs; BMP4; bone morphogenetic protein 4; C57BL/6; C57BL/6 mouse; CM; conditioned medium; DAPI; 4â²,6-diamidino-2
EB2017-Progress in Epidermolysis Bullosa Research toward Treatment and Cure
Keywords: گوسفند اپیدرمولیز; BMT; bone marrow transplantation; DEB; dystrophic epidermolysis bullosa; DEBRA; Dystrophic Epidermolysis Bullosa Research Association; EB; epidermolysis bullosa; EBS; epidermolysis bullosa simplex; JEB; junctional epidermolysis bullosa; PTC; premature ter
Bone Marrow-Derived Stem Cells Migrate into Intraepidermal Skin Defects of a Desmoglein-3 Knockout Mouse Model but Preserve their Mesodermal Differentiation
Keywords: گوسفند اپیدرمولیز; BMC; bone marrow cell; BMT; bone marrow transplantation; Dsg3; desmoglein-3; EB; epidermolysis bullosa; HSC; hematopoietic stem cell; JEB; junctional EB; MSC; mesenchymal stromal cell; PBS; phosphate buffered saline; RDEB; recessive dystrophic EB;
Cardiomyopathy in Patients With Hereditary Bullous Epidermolysis
Keywords: گوسفند اپیدرمولیز; Echocardiography; Epidermolysis bullosa; Micronutrients; Dilated cardiomyopathy; Ecocardiograma; Epidermólisis ampollosa; Micronutrientes; MiocardiopatÃa dilatada;
MiocardiopatÃa en pacientes con epidermólisis ampollosa hereditaria
Keywords: گوسفند اپیدرمولیز; Ecocardiograma; Epidermólisis ampollosa; Micronutrientes; MiocardiopatÃa dilatada; Echocardiography; Epidermolysis bullosa; Micronutrients; Dilated cardiomyopathy;
ReviewMolecular pathology of the basement membrane zone in heritable blistering diseases:: The paradigm of epidermolysis bullosa
Keywords: گوسفند اپیدرمولیز; Epidermolysis bullosa; Heritable blistering diseases; Cutaneous basement membrane zone; Type VII collagen;
Monoallelic Large Intragenic KRT5 Deletions Account for Genetically Unsolved Cases of Epidermolysis Bullosa Simplex
Keywords: گوسفند اپیدرمولیز; EB; epidermolysis bullosa; EBS; epidermolysis bullosa simplex;
Mutations in KLHL24 Add to the Molecular Heterogeneity of Epidermolysis Bullosa Simplex
Keywords: گوسفند اپیدرمولیز; EB; epidermolysis bullosa; EBS; epidermolysis bullosa simplex; KLHL24; Kelch-like family member 24; KRT14; keratin 14;
Epidermolysis bullosa pruriginosa a clinico-pathological study in an index case, highlighting its affliction in 11 of 27 member of the family
Keywords: گوسفند اپیدرمولیز; Epidermolysis bullosa; Hallopeau-Siemens; Dystrophic epidermolysis bullosa;
ReviewCell therapy for basement membrane-linked diseases
Keywords: گوسفند اپیدرمولیز; BM; basement membrane; BMT; bone marrow transplantation; EB; epidermolysis bullosa; DEB; dystrophic epidermolysis bullosa; HSCs; hematopoietic stem cells; iPSCs; induced pluripotent stem cells; JEB; junctional epidermal bullosa; MSCs; mesenchymal stromal
Dystrophic Epidermolysis Bullosa: COL7A1 Mutation Landscape in a Multi-Ethnic Cohort of 152 Extended Families with High Degree of Customary Consanguineous Marriages
Keywords: گوسفند اپیدرمولیز; DEB; dystrophic epidermolysis bullosa; EB; epidermolysis bullosa; Mb; mega-base pair; NGS; next-generation sequencing; RDEB; recessive dystrophic EB; SNP; single nucleotide polymorphism; WES; whole-exome sequencing;
Amlexanox Enhances Premature Termination Codon Read-Through in COL7A1 and Expression of Full Length Type VII Collagen: Potential Therapy for Recessive Dystrophic Epidermolysis Bullosa
Keywords: گوسفند اپیدرمولیز; DEJ; dermal-epidermal junction; EB; epidermolysis bullosa; NMD; nonsense mediated mRNA decay; PTC; premature termination codon; RDEB; recessive dystrophic epidermolysis bullosa;
Pro-Inflammatory Chemokines and Cytokines Dominate the Blister Fluid Molecular Signature in Patients with Epidermolysis Bullosa and Affect Leukocyte and Stem Cell Migration
Keywords: گوسفند اپیدرمولیز; ADSC; adipose-derived stem cell; BF; blister fluid; BMZ; basement membrane zone; DEB; dystrophic epidermolysis bullosa; EB; epidermolysis bullosa; EBS; epidermolysis bullosa simplex; JEB; junctional epidermolysis bullosa; MMP; matrix metalloproteinase; PB
KRT5 and KRT14 Mutations in Epidermolysis Bullosa Simplex with Phenotypic Heterogeneity, and Evidence of Semidominant Inheritance in a Multiplex Family
Keywords: گوسفند اپیدرمولیز; EBS; epidermolysis bullosa;
Progress toward Treatment and Cure of Epidermolysis Bullosa: Summary of the DEBRA International Research Symposium EB2015
Keywords: گوسفند اپیدرمولیز; BM; bone marrow; BMT; bone marrow transplantation; DEB; dystrophic EB; EB; epidermolysis bullosa; HMGB1; high mobility group box 1; iPSCs; inducible pluripotent stem cells; JEB; junctional EB; MSC; mesenchymal stromal/stem cell; RDEB; recessive DEB; SCC;
The p.Glu477Lys Mutation in Keratin 5 Is Strongly Associated with Mortality in Generalized Severe Epidermolysis Bullosa Simplex
Keywords: گوسفند اپیدرمولیز; EB; epidermolysis bullosa; GS-EBS; generalized severe epidermolysis bullosa simplex;
Estrategias terapéuticas innovadoras para la epidermólisis bullosa distrófica recesiva
Keywords: گوسفند اپیدرمولیز; Genodermatosis; Epidermólisis bullosa; Terapias avanzadas; GenéticaGenodermatosis; Epidermolysis bullosa; Advanced therapies; Genetics
Herlitz epidermolysis bullosa in the paediatric patient: Anaesthetic implications
Keywords: گوسفند اپیدرمولیز; Epidermolysis Bullosa; Anesthesia; Infant, Newborn; Anestesiology; Perioperative PeriodEpidermolisis ampollosa; Anestesia; Recién nacido; Anestesiología; Periodo perioperatorio
Stomatologic management of dental malocclusion in patients with dystrophic epidermolysis bullosa using an interceptive guide of occlusion (IGO): Comparison of two cases
Keywords: گوسفند اپیدرمولیز; Epidermolysis bullosa; serial extraction; microstomia; stomatologic management; guide of occlusion; Epidermólisis bullosa; extracción seriada; microstomÃa; manejo estomatológico; guÃa de la oclusión;
Host–pathogen interactions in epidermolysis bullosa patients colonized with Staphylococcus aureus
Keywords: گوسفند اپیدرمولیز; Epidermolysis bullosa; Staphylococcus aureus; Wound; Colonization
Development, reliability, and validity of a novel Epidermolysis Bullosa Disease Activity and Scarring Index (EBDASI)
Keywords: گوسفند اپیدرمولیز; epidermolysis bullosa; Epidermolysis Bullosa Disease Activity and Scarring Index; outcome measure; reliability; severity score; validation; BEBS; Birmingham Epidermolysis Bullosa Severity; CI; confidence interval; EB; epidermolysis bullosa; EBDASI; Epider
Analysis of chemotactic molecules in bone marrow-derived mesenchymal stem cells and the skin: Ccl27-Ccr10 axis as a basis for targeting to cutaneous tissues
Keywords: گوسفند اپیدرمولیز; adult stem cells; blistering skin; chemokine receptors; chemokines; epidermolysis bullosa; gene expression analysis; mesenchymal stem cells; migration; transplantation;
The largest family of the Americas with dominant dystrophic epidermolysis bullosa pruriginosa: A 18-year longitudinal genotype-phenotype study
Keywords: گوسفند اپیدرمولیز; EB; Epidermolysis bullosa; Pruriginosa; Mutation; Genotype; Phenotype;
Genodermatoses
Keywords: گوسفند اپیدرمولیز; cancer syndromes; collagen; epidermolysis bullosa; filaggrin; genodermatoses; ichthyosis; keratinization; pseudoxanthoma elasticum; vascular anomalies
Dystrophic Epidermolysis Bullosa in Goats
Keywords: گوسفند اپیدرمولیز; anchoring fibrils; basal membrane; epidermolysis bullosa; goat