
In vivo experimental evidence that the major metabolites accumulating in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency induce oxidative stress in striatum of developing rats: A potential pathophysiological mechanism of striatal damage in this disorder
Keywords: اسید ترشکلراکتیک; CAT; catalase; DCF; 2â²,7â²-dichlorofluorescein; DCFH; 2â²,7â²-dichloroflurescin; DCFH-DA; 2â²,7â²-dichlorofluorescin diacetate; DNPH; 2,4-dinitrophenylhydrazine; GC/MS; gas chromatography/mass spectrometry; G6PD; glucose-6-phosphate dehydrogenase;