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در این صفحه تعداد 295 مقاله تخصصی درباره هستند که در نشریه های معتبر علمی و پایگاه ساینس دایرکت (Science Direct) منتشر شده، نمایش داده شده است. برخی از این مقالات، پیش تر به زبان فارسی ترجمه شده اند که با مراجعه به هر یک از آنها، می توانید متن کامل مقاله انگلیسی همراه با ترجمه فارسی آن را دریافت فرمایید.
در صورتی که مقاله مورد نظر شما هنوز به فارسی ترجمه نشده باشد، مترجمان با تجربه ما آمادگی دارند آن را در اسرع وقت برای شما ترجمه نمایند.
مقالات ISI هستند (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; GD; Gaucher disease; GCase; β-glucocerebrosidase; GC; β-glucosylceramide; PD; Parkinson disease; ERT; enzyme-replacement therapy; GBA; glucocerebrosidase gene; GBA-EMI; GBA expected mutation impact; ER; endoplasm reticulum; DCs; dendritic-cells; NKT; na
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; ERT; enzyme replacement therapy; ACP; acid phosphatase; ACE; angiotensin converting enzyme; GC; Gaucher cells; GD2; Gaucher disease Type 2; Neuronopathic Gaucher disease; Pulmonary involvement; Myelodysplastic syndrome; Autopsy; CD68 immune staining;
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; formulation; pharmacokinetics; liposomes; proteins; pharmacodynamics; rhGAA; recombinant human acid α-glucosidase; PI; phosphatidylinositol; FVIII; factor VIII; GAA; acid α-glucosidase; 4-MUG; 4-methylumbelliferyl-α-d-glucopyranoside; PI-rhGAA; PI lipo
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; Glucocerebrosidase deficiency; Lysosomal storage disease; Resting energy expenditure; Insulin resistance; High-density lipoprotein cholesterol; Hepatocellular carcinoma; Gaucher disease; ApoAI; apolipoprotein AI; ApoB; apolipoprotein B; ApoE; apolipoprote
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; ALB; albumin; AST; aspartate aminotransferase; CK; creatine kinase; Cort-FZ; faecal cortisol; Cort-SG; blood cortisol; ERT; erythrocyte; ALP; alkaline phosphatase; FLAG; flag handling; FrAm; fructosamine; GLI; glucose; Hb; haemoglobin; LEU; leukocytes; LI
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; DD; Gaucher disease; ERT; enzyme replacement therapy; FDA; Food and Drug Administration; AST; aspartate aminotransferase; ALT; alanine aminotransferase; SOC; System Organ Classification; Gaucher disease; Lysosomal storage diseases; Enzyme replacement ther
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; Fabry disease; Diagnosis; Mutation; Management; Treatment; ACEI; angiotensin converting enzyme inhibitor; ARB; angiotensin receptor blocker; AV; atrioventricular; α-Gal A; α-galactosidase A; CKD; chronic kidney disease; CNS; central nervous system; CT;
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; Fabry; Cardiomyopathy; Echocardiography; CS; Circumferential strain; DTI; Doppler tissue imaging; ERT; Enzyme replacement therapy; HCM; Hypertrophic cardiomyopathy; LS; Longitudinal strain; LV; Left ventricular; LVEF; Left ventricular ejection fraction; L
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; ADA; anti-drug antibodies; AMPK; 5′ adenosine monophosphate-activated protein kinase; aHUS; atypical hemolytic uremic syndrome; AMD; age-related macular degeneration; APC; antigen presenting cells; AT; anaphylatoxin; BTK; Bruton's tyrosine kinase; C1q
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; Decentralized clinical trial; eHealth; Patient-centric trial; Access to trials; Recruitment; ERT; eResearchTechnology; eDiary; electronic diary; eICF; electronic Informed Consent Form; ePRO; electronic patient reported outcomes; RCTs; randomized clinical
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; 6BDT; 6 Blade Disc Turbine (Rushton Turbine); 6MFD; 6 mixed flow downward pumping; 6MFU; 6 mixed flow upward pumping; DAS; data acquisition system; DGD; dynamic gas disengagement; ERT; electrical resistance tomography; FEM; finite element method; ITS; Ind
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; Lysosomal acid lipase deficiency; Cholesteryl ester storage disease (CESD); Wolman disease; Liver failure; Liver transplantation; Enzyme replacement therapy; Lysosomal storage disease; LAL-D; Lysosomal acid lipase deficiency; LSD; lysosomal storage diseas
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; ERT; Enzyme replacement therapy; NC; Neurocysticercosis; cS3PvacTL; S3Pvac transplastomic line; S4PvacTL; S4Pvac transplastomic line; Taenia solium; Chloroplast expression; Polycistron; S3Pvac vaccine; Plant-based vaccine;
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; Case report; Elosulfase alfa; Enzyme replacement therapy; Morquio A syndrome; Mucopolysaccharidosis type IV A; Non-ambulatory; ERT; enzyme replacement therapy; GAG; glycosaminoglycan; GALNS; N-acetylgalactosamine-6-sulfatase; KS; keratan sulfate; 3MSCT; 3
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; CNS; central nervous system; ERT; Enzyme replacement therapy; HCT; hematopoietic cell transplantation; MPS; Mucopolysaccharidosis; MPS I; Mucopolysaccharidosis Type I; MPS IH; Mucopolysaccharidosis Type IH, Hurler Syndrome; MRI; magnetic resonance imaging
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; CNS; central nervous system; CSF; cerebrospinal fluid; EDS; excessive daytime sleepiness; EHR; electronic health record; ERT; emergency response team; OSA; obstructive sleep apnea; REM; rapid eye movement; Emergency response teams; General anesthesia; Hem
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; BMD; bone mineral density; ECG; electrocardiogram; ERT; enzyme replacement therapy; ICGG; International Collaborative Gaucher Group; Type 1 Gaucher disease; Eliglustat; Substrate reduction therapy; Enzyme replacement/augmentation therapy; Drug metabolism;
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; ERT; Enzyme replacement therapy; GAA; α-glucosidase; IMST; Inspiratory muscle strength training; LC; Load compensation; MIP; Maximal inspiratory pressure; MRI; Magnetic resonance imaging; MV; Mechanical ventilation; Pompe disease; Diaphragm; Gene therapy
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; ERT; enzyme replacement therapy; Gb3; Globotriaosylceramide; IVSd; diastolic interventricular septal thickness; LOD; limit of detection; LVIDd; diastolic left ventricular internal diameter; LVIDs; systolic left ventricular internal diameter; LVM; left ven
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; ALT; alanine aminotransferase; bw; body weight; CESD; cholesteryl ester storage disease; EC; esterified cholesterol; E/L; endosomal/lysosomal; ERT; enzyme replacement therapy; Fas; fatty acid synthase; Hmgcr; hydroxymethylglutaryl coenzyme A reductase; Hm
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; Salinity; Macropores; Preferential flow; Reclamation; Remediation; Tile drains; AES; atomic emission spectroscopy; bgs; below ground surface; EC; electrical conductivity; ERT; electrical resistivity tomography; ET; evapotranspiration; FAO; Food and Agricu
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; ACSF; artificial cerebrospinal fluid; BL; baseline; CNS; central nervous system; CON-MOCK; mock-treated control mice; CA; cornu ammonis; DG; dentate gyrus; ERT; enzyme replacement therapy; FAD; familial Alzheimer's disease; fEPSPs; field excitatory postsy
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; Lysosomal Storage Disorders; Oxidative stress; Reactive species; Oxidative damage; 4-HNE; 4-hydroxynonenal; 7-KC; 7-ketocholesterol; 8-OHdG; 8-hydroxy-2′-deoxyguanosine; AGE; advanced glycation end product; BD; Batten disease; Ca2 +;  calcium; CAT; ca
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; AAV; adeno-associated viruses; AE; adverse event; BBB; blood-brain barrier; CLN2; ceroid lipofuscinosis neuronal type 2; CNS; central nervous system; CSF; cerebrospinal fluid; DQ; developmental quotient; ERT; enzyme replacement therapy; g7; 7-aminoacid gl
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; LSD; lysosomal storage disease; CNS; central nervous system; BBB; blood-brain barrier; ERT; enzyme replacement therapy; GAG; glycosaminoglycans; CSF; cerebrospinal fluid; FDA; food and drug administration; ICV; intracerebroventricular; HLA; human leukocyt
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; ER; endoplasmic reticulum; ERT; enzyme replacement therapy; FDA; U.S. Food and Drug Administration; LD; lysosomal disease; M6P; mannose-6-phosphate; M6PR; mannose-6-phosphate receptor; MPS; mucopolysaccharidosis; NPC; Type C Niemann-Pick disease; NPD; Typ
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; Estrogens; Progesterone; Menopause; Hormone replacement therapy; Sleep loss; Memory; Executive function; Primate; Rodent; Human; 5-CSRTT; 5-choice serial reaction time test; Aβ; β-amyloid; AD; Alzheimer's disease; DMP; delayed matching-to-position; DN
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; α-gal A; α-galactosidase A; Cr; creatinine; ERT; enzyme replacement therapy; FD; Fabry disease; GCL; glutamate cysteine ligase; Gb3; globotriaosylceramide; GLA; α-galactosidase A coding gene; GPx; glutathione peroxidase; GR; glutathione reductase; GSH;
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; α-Gal A; alpha-galactosidase A; CKD EPI; Chronic Kidney Disease Epidemiology Collaboration; eGFR; estimated glomerular filtration rate; ERT; enzyme replacement therapy; FOS; Fabry Outcome Survey; LVH; left ventricular hypertrophy; LVMI; left ventricular
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; ADA; anti-drug antibody; AE; adverse event; CCL18; chemokine (C-C motif) ligand 18; ECL; electrochemiluminescence; ELISA; enzyme-linked immunosorbent assay; ERT; enzyme replacement therapy; GD; Gaucher disease; RIP; radioimmunoprecipitation; TEAE; treatme
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; ANOVA; one-way analysis of variance; BMD; bone mineral density; BMI; body mass index; CCL18; chemokine (C-C motif) ligand 18; EC; Enzyme commission number; ERT; enzyme replacement therapy; GBA; glucocerebrosidase; GD; Gaucher disease; DXA; dual energy X-r
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; Gaucher disease; Splenectomy; Immunophenotyping; Lymphocyte subsets; Dendritic cells; Comorbidities; CBC; complete blood count; COPD; chronic obstructive pulmonary disease; DC; dendritic cells; ERT; Enzyme replacement therapy; GD; Gaucher disease; HC; hea
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; DAS; Difficult Airway Society; ERT; Enzyme replacement therapy; GAGs; Glycosaminoglycans; HSCT; Hematopoietic stem cell transplantation; MPS; Mucopolysaccharidosis; QoL; Quality of life; Mucopolysaccharidoses; Adult; Disease management; Lysosomal storage
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; EMG; electromyography; ERT; estimated resting twitch amplitude; I100; 100% of the intensity to elicit MEPs of maximal amplitude at 20% MVC; I75; 75% of the intensity to elicit MEPs of maximal amplitude at 20% MVC; I50; 50% of the intensity to elicit MEPs
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; cardiac fibrosis; IVS4+919G>A; late gadolinium enhancement; newborn screening; CAD; coronary artery disease; ERT; enzyme replacement therapy; FD; Fabry disease; Gal A; galactosidase A; Gb3; globotriaosylceramide; GE-CMR; gadolinium-enhanced cardiac magnet
Elsevier - ScienceDirect - الزویر - ساینس دایرکت
Keywords: هستند; 3MSCT; 3-minute stair climb test; 6MWT; 6-minute walk test; AE; adverse event; ERT; enzyme replacement therapy; GALNS; enzyme N-acetylgalactosamine-6-sulfatase; IAR; infusion-associated reaction; IgE; immunoglobulin E; ITT; intent-to-treat; KS; keratan su