Keywords: بیماری هیرشپرونگ; Ayurveda; Erandmooladi yapna basti; Hirschsprung disease; Matra basti; Pakvasayagata vata;
مقالات ISI بیماری هیرشپرونگ (ترجمه نشده)
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Keywords: بیماری هیرشپرونگ; CI; confidence interval; dGIF; distant Genealogic Index of Familiality; HSCR; Hirschsprung disease; GIF; Genealogic Index of Familiality; ICD; International Classification of Diseases; IM; Intermountain Healthcare; RR; relative risk; MEN-IIa; multiple end
Keywords: بیماری هیرشپرونگ; Anorectal malformation; Hirschsprung disease; Sexual functioning; Psychosocial problems;
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Neuron development; Therapeutic drugs; Microarray; Connectivity Map;
Keywords: بیماری هیرشپرونگ; Pediatric surgery; Anorectal malformation; Imperforate anus; Hirschsprung disease; Transitions in care; Delivery of care;
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Duhamel operation; Functional outcomes;
Keywords: بیماری هیرشپرونگ; PSARP; Posterior sagittal anorectoplasty; HD; Hirschsprung disease; PT; Pull-through; Posterior sagittal anorectoplasty; Hirschsprung disease; Redo pull-through;
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Fecal incontinence; Constipation; Soiling; Bowel function; Quality of life;
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Incidence; Presentation; Management; Stoma;
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Laparoscopy; Transanal pull-through; Anorectal line; Dentate line;
Keywords: بیماری هیرشپرونگ; HD; Hirschsprung disease; RSB; Rectal suction biopsy; CIS; Calretinin immunohistochemical staining; RA; Residual aganglionosis; TZB; Transition zone bowel; Hirschsprung disease; Residual aganglionosis; Transition zone bowel; Rectal suction biopsy; Calreti
Keywords: بیماری هیرشپرونگ; Neonatal; Gastrointestinal; Intestinal atresia; Malrotation; Tracheoesophageal fistula; Pyloric stenosis; Hirschsprung disease; Meconium ileus;
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Rectal biopsy
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Constipation; Enteric nervous system; Myenteric plexus; Nitric oxide synthase; Calretinin;
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Chemically ablated enteric nervous system; Aganglionosis; Mouse model; Miniature endoscopy
Keywords: بیماری هیرشپرونگ; Anorectal malformation; Hirschsprung disease; Quality of life;
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Pullthrough; Anorectal malformation; Anorectoplasty; Ileal pouch anal anastomosis; Complications;
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Urological outcome; Sexual outcome; Systematic review;
Keywords: بیماری هیرشپرونگ; Evidence-based medicine; upper gastrointestinal tract; lower gastrointestinal tract; small bowel obstruction; large bowel obstruction; diagnosis; sensitivity and specificity; confidence interval; duodenal atresia; duodenal stenosis; jejunal atresia; ileal
Keywords: بیماری هیرشپرونگ; HSCR; Hirschsprung disease; CNV; copy number variation; LOH; loss of heterozygosity; qPCR; quantitative polymerase chain reaction; S-HSCR; short-segment Hirschsprung disease; L-HSCR; long-segment Hirschsprung disease; TCA; total colonic aganglionosis; SNP
Keywords: بیماری هیرشپرونگ; Enteric nervous system; Enteric neuropathies; Stem cells; Cell replacement therapy; Hirschsprung disease;
Keywords: بیماری هیرشپرونگ; Short bowel syndrome; Intestinal dysmotility; Hirschsprung Disease; Anorectal malformation; Continuity of care; Transitional care
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Contrast enema; Barium enema
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Children; The transanal endorectal descent; EnterocolitisEnfermedad de Hirschsprung; Niños; Descenso endorrectal transanal; Enterocolitis
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Anal endosonography; Anal manometry; Anal sphincter; Postoperative fecal incontinence;
Keywords: بیماری هیرشپرونگ; Markov chain model; Agent-based model; Incomplete penetrance; Hirschsprung Disease;
Keywords: بیماری هیرشپرونگ; degenerative leiomyopathy; dysmotility; enteric muscle; enteric nervous system; ganglioneuromatosis; Hirschsprung disease; pseudo-obstruction;
Keywords: بیماری هیرشپرونگ; child; fecal incontinence; Hirschsprung disease; retrospective study; total colonic aganglionosis
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Reoperation; Pullthrough; Aganglionosis; Enterocolitis; Stricture; Endorectal pullthrough
Keywords: بیماری هیرشپرونگ; Congenital abnormalities; Neonatal intestinal obstruction; Hirschsprung disease; Anorectal malformation;
Keywords: بیماری هیرشپرونگ; Age at presentation; Intussusception; Pyloric stenosis; Inguinal hernia; Malrotation; Hirschsprung disease;
Keywords: بیماری هیرشپرونگ; Fetus; ZEB2 gene mutation; Fetoxpathological examination; Hirschsprung disease; Corpus callosum hypoplasia;
Keywords: بیماری هیرشپرونگ; Leukodystrophy; Mitochondrial disease; Crohn disease; Hirschsprung disease; Myopathy; Ganglion cell; Intestinal pseudo-obstruction;
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Rare variants; GWAS; Next generation sequencing; Systems biology; Functional assays;
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Transition zone; Nerve hypertrophy; Aganglionosis
Keywords: بیماری هیرشپرونگ; neonate; emesis; emergency department; newborn; pyloric stenosis; gastrointestinal; gastroesophageal reflux; gastroesophageal reflux disease; malrotation; volvulus; intestinal atresia; Hirschsprung disease; incarcerated hernia; necrotizing enterocolotis
Combined genetic effects of RET and NRG1 susceptibility variants on multifactorial Hirschsprung disease in Indonesia
Keywords: بیماری هیرشپرونگ; Common variants; Combined effect; Hirschsprung disease; Indonesia; NRG1; RET;
Increased expression of Semaphorin 3A in the endothelin receptor-B null mouse model of Hirschsprung disease
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Enteric neural crest-derived cell; Enteric nervous system; Sox10-Venus mice; Semaphorin 3A;
GT-repeat extension in the IL11 promoter is associated with Hirschsprung's disease (HSCR)
Keywords: بیماری هیرشپرونگ; AGT; angiotensinogen; ALDH2; dehydrogenase 2; APC; antigen-presenting cell; CD11c; cluster of differentiation 11c; CI; confidence interval; COPD; chronic obstructive pulmonary disease; CLL; chronic lymphocytic leukemia; DENND3; DENN domain containing prot
Reduction of hydrogen sulfide synthesis enzymes cystathionine-β-synthase and cystathionine-γ-lyase in the colon of patients with Hirschsprungs disease
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; Hirschsprung associated enterocolitis (HAEC); Cystathionine-β-synthase (CBS); Cystathionine-γ-lysase (CSE);
Diagnostic Role of Anal Sphincter Relaxation Integral in High-Resolution Anorectal Manometry for Hirschsprung Disease in Infants
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; conventional anorectal manometry; high-resolution anorectal manometry; anal sphincter relaxation integral; ARM; Anorectal manometry; ASRI; Anal sphincter relaxation integral; AUC; Area under the curve; HRAM; High-resolution anorectal
Duhamel operation vs. transanal endorectal pull-through procedure for Hirschsprung disease: A systematic review and meta-analysis
Keywords: بیماری هیرشپرونگ; Duhamel operation; Transanal endorectal pull-through procedure; TERPT; Hirschsprung disease; Fecal incontinence;
Identification of Variants in RET and IHH Pathway Members in a Large Family With History of Hirschsprung Disease
Keywords: بیماری هیرشپرونگ; ENS; Neural Development; Genetic Causes of HSCR; Family Study; bp; base pair; ENS; enteric nervous system; GDNF; glial cell-derived neurotrophic factor; GFP; green fluorescent protein; GLI1; GLI family zinc finger 1; GLI3; GLI family zinc finger 3; HEK;
CAPS PaperAntegrade continence enemas improve quality of life in patients with medically-refractory encopresis
Keywords: بیماری هیرشپرونگ; ACE; Antegrade continence enema; ARM; Anorectal malformation; HD; Hirschsprung Disease; QOL; Quality of life; Encopresis; Antegrade continence enema (ACE);
ClinicalRedo pull-through surgery in Hirschsprung disease: Short-term clinical outcome
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; TERPT; Redo surgery; Redo pull-through; Transition zone;
Original ArticleLong-term results of the Duhamel technique are superior to those of the transanal pullthrough: A study of fecal continence and quality of life
Keywords: بیماری هیرشپرونگ; Fecal continence; Quality of life; Validation of questionnaire; Hirschsprung disease; Transanal pull-through; Aganglionosis;
Operative TechniqueSurgical approach for fecal incontinence with a patulous anus after transanal pull-through for Hirschsprung disease
Keywords: بیماری هیرشپرونگ; TAPT; transanal pull-through; HD; Hirschsprung disease; JSGA; Japanese Study Group of Anorectal Anomalies; 3D; three-dimensional; Hirschsprung disease; Transanal endorectal pull-through operation; Fecal incontinence; Anal canal plasty;
Clinical PaperSingle-stage transanal endorectal pull-through procedure for correction of Hirschsprung disease in neonates and nonneonates: A multicenter study
Keywords: بیماری هیرشپرونگ; Neonate; Nonneonate; Single-stage transanal endorectal pull-through (SSTEPT); Hirschsprung disease; Outcome;
Clinical PaperPatient-reported Swedish nationwide outcomes of children and adolescents with total colonic aganglionosis
Keywords: بیماری هیرشپرونگ; Total colonic aganglionosis; Hirschsprung disease; Bowel function; Nutrition;
Basic Science PaperUpregulation of MiR-369-3p suppresses cell migration and proliferation by targeting SOX4 in Hirschsprung's disease
Keywords: بیماری هیرشپرونگ; Hirschsprung disease; miRNAs; Neural crest cell; Gastroenterology; Congenital diseases;