Keywords: بیماری هانتینگتون; Huntington's disease; Parkinson's disease; Cognition; Review; 6-OHDA; MPTP; Behaviour; Phenotype; Cognitive tests; Basal ganglia; Corticostriatal; Dopamine;
مقالات ISI بیماری هانتینگتون (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: بیماری هانتینگتون; Functional connectivity; Cognition; Executive function; Cortical networks; Huntington's disease; Neurodegeneration; fMRI;
Keywords: بیماری هانتینگتون; Huntington's disease; Transcranial magnetic stimulation; Electroencephalography; Cortical inhibition; GABA; Corticostriatal circuitry; Biomarker;
Keywords: بیماری هانتینگتون; Parkinson's disease; Huntington's disease; Neurodegenerative diseases; Mitochondrial dysfunction; Creatine; Co-Q10; PGC-1α; Sirtuins;
Keywords: بیماری هانتینگتون; Huntington's disease; Induced pluripotent stem cells; IPSC; MSN; Stem cell models; Neurodegenerative disease;
Keywords: بیماری هانتینگتون; Huntington's disease; Caffeine; Adenosine receptors;
Keywords: بیماری هانتینگتون; AD; Alzheimer's disease; CR; caloric restriction; DRG; dorsal root ganglion; Drp1; dynamin-related protein 1; HAT; histone acetyltransferase; HD; Huntington's disease; HDAC; histone deacetylase; Hsp90; heat shock protein 90; KAT; lysine acetyltransferases
Keywords: بیماری هانتینگتون; Huntington's disease; Yoga; Qualitative; Exercise; Mindfulness; Physiotherapy;
Normalizing glucocorticoid levels attenuates metabolic and neuropathological symptoms in the R6/2 mouse model of huntington's disease
Keywords: بیماری هانتینگتون; Glucocorticoids; Corticosterone; Huntington's disease; Metabolism; Indirect calorimetry; Cachexia; Neuropathology; Neurogenesis; Inclusion bodies; R6/2 mouse;
Drp1 phosphorylation by MAPK1 causes mitochondrial dysfunction in cell culture model of Huntington's disease
Keywords: بیماری هانتینگتون; Mitochondrial fission; Dynamin-related protein 1; Mitogen-activated protein kinase 1; Huntington's disease; Phosphorylation;
Identification of pseudobulbar affect symptoms in the nursing home setting: Development and assessment of a screening tool
Keywords: بیماری هانتینگتون; Pseudobulbar affect; Nursing home; Screening; Dextromethorphan hydrobromide/quinidine sulfate; Long-term care; ALS; Amyotrophic lateral sclerosis; BIMS; Brief Interview for Mental Status; CP; consultant pharmacists; DM/Q; dextromethorphan hydrobromide/qui
Beta catenin is regulated by its subcellular distribution and mutant huntingtin status in Huntington's disease cell STHdhQ111/HdhQ111
Keywords: بیماری هانتینگتون; Beta catenin; Huntington's disease; MicroRNA-214; Mutant huntingtin; STHdhQ111/HdhQ111; BDNF; Brain Derived neurotrophic factor; HD; Huntington's Disease; Htt; Huntingtin (mouse); HYPK; Huntingtin Yeast Partner K; miR-214; MicroRNA-214; snRNA; Small Nucle
Topiramate mitigates 3-nitropropionic acid-induced striatal neurotoxicity via modulation of AMPA receptors
Keywords: بیماری هانتینگتون; GluR2; AMPA; Topiramate; 3-Nitropropionic acid; Excitotoxicity; Huntington's disease;
Extrastriatal degeneration correlates with deficits in the motor domain subscales of the UHDRS
Keywords: بیماری هانتینگتون; Huntington's disease; Voxel-based morphometry; UHDRS; MRI; Basal ganglia;
Maternal exposure to nonylphenol during pregnancy and lactation induces microglial cell activation and pro-inflammatory cytokine production in offspring hippocampus
Keywords: بیماری هانتینگتون; AD; Alzheimer's disease; AP-1; activator protein 1; BBB; blood-brain barrier; BPA; bisphenol A; CNS; central nervous system; COX-2; cyclooxygenase-2; DAPI; 4â²,6âdiamidinoâ2âphenylindole; EDC; endocrine disrupting chemical; ELISA; enzyme-linked imm
Suicidal ideation and suicidal behavior according to the C-SSRS in a European cohort of Huntington's disease gene expansion carriers
Keywords: بیماری هانتینگتون; Huntington's disease; Suicidal ideation; Suicidal behavior; Columbia-Suicide Severity Rating Scale;
Therapeutic efficacy of regulable GDNF expression for Huntington's and Parkinson's disease by a high-induction, background-free “GeneSwitch” vector
Keywords: بیماری هانتینگتون; GeneSwitch; Regulated expression; GDNF; Parkinson's disease; Huntington's disease; AAV; Mifepristone;
Diminished facial EMG responses to disgusting scenes and happy and fearful faces in Huntington's disease
Keywords: بیماری هانتینگتون; Huntington's disease; Facial EMG; Emotion processing; Facial mimicry; Emotion recognition; Disgust; corr; corrugator supercilii; DBS; Disease Burden Score; fron; frontalis; IAPS; International Affective Picture System; lev; levator labii; orbi; orbiculari
Polyglutamine repeat proteins disrupt actin structure in Drosophila photoreceptors
Keywords: بیماری هانتینگتون; Actin; Drosophila; Huntington's disease; Photoreceptor; Formin; Polyglutamine;
Prospective evaluation of Globus pallidus internus deep brain stimulation in Huntington's disease
Keywords: بیماری هانتینگتون; Huntington's disease; Chorea; Deep brain stimulation; Globus pallidus internus;
Designing aptamers which respond to intracellular oxidative stress and inhibit aggregation of mutant huntingtin
Keywords: بیماری هانتینگتون; Huntington's disease; Oxidative stress; Protein aggregation; Saccharomyces cerevisiae; Sensor;
The ubiquitin conjugating enzyme Ube2W regulates solubility of the Huntington's disease protein, huntingtin
Keywords: بیماری هانتینگتون; Huntington's disease; Huntingtin; Ubiquitination; Ubiquitin-conjugating enzyme; Ube2W; Protein misfolding; Neurodegeneration;
Huntingtin protein: A new option for fixing the Huntington's disease countdown clock
Keywords: بیماری هانتینگتون; Huntingtin; Aptamers; Biophysics; Huntington's disease; Oligonucleotide;
CYP46A1 protects against NMDA-mediated excitotoxicity in Huntington's disease: Analysis of lipid raft content
Keywords: بیماری هانتینگتون; Excitotoxicity; CYP46A1; Huntington's disease; Lipid rafts; GluN2B; Cholesterol;
Perturbations in the p53/miR-34a/SIRT1 pathway in the R6/2 Huntington's disease model
Keywords: بیماری هانتینگتون; Huntington's disease; miR-34a; SIRT1; p53;
The small heat shock proteins, especially HspB4 and HspB5 are promising protectants in neurodegenerative diseases
Keywords: بیماری هانتینگتون; α-Crystallins; Neurodegenerative diseases; Neuroprotection; Gene regulation; Aβ; β-amyloid peptides; AD; Alzheimer's disease; ALS; Amyotrophic lateral sclerosis; AxD; Alexander's disease; CNS; Central nervous system; EAE; experimental autoimmune enceph
Pramipexole reduces soluble mutant huntingtin and protects striatal neurons through dopamine D3 receptors in a genetic model of Huntington's disease
Keywords: بیماری هانتینگتون; Huntington's disease; Neurodegeneration; Neuroprotection; D3 receptor; Autophagy;
Diarylcyclopropane hydroxamic acid inhibitors of histone deacetylase 4 designed by combinatorial approach and QM/MM calculations
Keywords: بیماری هانتینگتون; Huntington's disease; Histone deacetylases; Inhibitors of HDAC4; Computer-assisted drug design; QM/MM approach; B3LYP; hybrid gradient-corrected exchange-correlation functional of electron density; CADD; computer-assisted drug design; DCHA; trans-(2R,3R)-
Bilateral quinolinic acid-induced lipid peroxidation, decreased striatal monoamine levels and neurobehavioral deficits are ameliorated by GIP receptor agonist D-Ala2GIP in rat model of Huntington's disease
Keywords: بیماری هانتینگتون; D-Ala2GIP; (Pro3)GIP; Quinolinic acid; Huntington's disease; Redox;
Aberrant subcellular localization of SQSTM1/p62 contributes to increased vulnerability to proteotoxic stress recovery in Huntington's disease
Keywords: بیماری هانتینگتون; ATF4; activating transcription factor 4; BSA; bovine serum albumin; CHX; cycloheximide; CQ; hydroxychloroquine; HD; Huntington's disease; HDAC6; histone deacetylase 6; Htt; huntingtin; mHtt; mutant huntingtin; Lamp1; lysosomal associated membrane protein
Prenatal exposure to benzophenone-3 (BP-3) induces apoptosis, disrupts estrogen receptor expression and alters the epigenetic status of mouse neurons
Keywords: بیماری هانتینگتون; Actb; β-actin; Aβ; amyloid beta; AD; Alzheimer's disease; ANOVA; analysis of variance; ASD; autism spectrum disorder; BP-3; benzophenone-3; BPA; bisphenol A; BPs; benzophenones; BSA; bovine serum albumin; Casp3; caspase-3; CNS; central nervous system; D
Sirtuin activators and inhibitors: Promises, achievements, and challenges
Keywords: بیماری هانتینگتون; CR; calorie restriction; DHP; 1,4-dihydropyridine; ECS; extended C-site; ELT; Encoded Library Technology; FdL; Fluor de Lys; HD; Huntington's disease; LPS; lipopolysaccharide; LDL; low density lipoprotein; MLS; mitochondrial localization sequences; NAM; n
Activation of NPY-Y2 receptors ameliorates disease pathology in the R6/2 mouse and PC12 cell models of Huntington's disease
Keywords: بیماری هانتینگتون; Aβ; beta-amyloid; ABC; avidin-biotin complex; BBB; blood brain barrier; BDNF; brain derived neurotrophic factor; BSA; bovine serum albumin; CREB; cAMP response element binding protein; cDNA; complementary deoxyribonucleic acid; DAB, 3; 3-diaminobenzidine
Neuroprotective effect of naringin, a flavone glycoside in quinolinic acid-induced neurotoxicity: Possible role of PPAR-γ, Bax/Bcl-2, and caspase-3
Keywords: بیماری هانتینگتون; Apoptosis; Huntington's disease; Mitochondrial complex; Naringin; Neuroinflammation; PPAR-γ; BAX; Bcl2 Associated X gene; FACS; Fluorescence-activated cell sorting; GSH; Reduced Glutathione; IL's; Interleukins; MDA; Malondialdehyde; MTT; 3-(4, 5-Dimethyl
Redox regulation of proteasome function
Keywords: بیماری هانتینگتون; Abcd1; ATP binding cassette subfamily D member 1; AD; Alzheimer's disease; ALD; adrenoleukodystrophy; ALS; amyotrophic lateral sclerosis; AP-1; activator protein-1; APP; amyloid precursor protein; CNS; central nervous system; DDI; DNA-damage inducible 1;
« Quand l'annonce du diagnostic médical devient un enjeu d'accompagnement. Enquête au sein du protocole du test présymptomatique de la maladie de Huntington »
Keywords: بیماری هانتینگتون; Accompagnement; Maladie de Huntington; Ãthique; Génétique; Présymptomatique; Supportive care; Huntington's disease; Ethical code; Genetic; Presymptomatic;
Research Paper2,4 DNP improves motor function, preserves medium spiny neuronal identity, and reduces oxidative stress in a mouse model of Huntington's disease
Keywords: بیماری هانتینگتون; DNP; 2,4-dinitrophenol; HD; Huntington's disease; mHtt; mutant huntingtin protein; ROS; reactive oxygen species; UCP; uncoupling protein; Mitochondrial uncoupling; 2,4-dinitrophenol; Oxidative stress, DARPP32; Huntington's disease;
Polyglutamine expansion of ataxin-3 alters its degree of ubiquitination and phosphorylation at specific sites
Keywords: بیماری هانتینگتون; Ataxin-3; Spinocerebellar ataxia type 3; Mass spectrometry; Neurodegeneration; Ubiquitination; Phosphorylation; DUB; deubiquitinating enzyme;; HD; Huntington's disease; HEK; human embryonic kidney;; LC-MS/MS; liquid chromatography tandem mass spectrometry
L-theanine prevent quinolinic acid induced motor deficit and striatal neurotoxicity: Reduction in oxido-nitrosative stress and restoration of striatal neurotransmitters level
Keywords: بیماری هانتینگتون; Catecholamines; Huntington's disease; GABA; Glutamate; Oxidative stress; L-theanine;
Extracellular matrix dynamics and functions in the social amoeba Dictyostelium: A critical review
Keywords: بیماری هانتینگتون; AcbA; acyl-CoA binding protein; AD; Alzheimer's disease; ALC; anterior-like cell; cAMP; cyclic adenosine monophosphate; CaBP; calcium-binding protein; Cad; calcium-dependent cell adhesion molecule; CaM; calmodulin; CaMBD; calmodulin-binding domain; CaMBP;
NeuropsiquiatrÃa de los trastornos del movimiento
Keywords: بیماری هانتینگتون; NeuropsiquiatrÃa; Trastornos del movimiento; Enfermedad de Parkinson; Enfermedad de Huntington; Circuitos; Frontosubcorticales; Neuropsychiatry; Movement disorders; Parkinson's disease; Huntington's disease; Circuits; Fronto-subcortical;
X-linked Dystonia-Parkinsonism patient cells exhibit altered signaling via nuclear factor-kappa B
Keywords: بیماری هانتینگتون; ANOVA; analysis of variance; AR; androgen receptor; DMEM; Dulbecco's modified Eagle's medium; DSC; disease-specific sequence change; ELISA; enzyme-linked immunosorbent assay; GLuc; Gaussia luciferase; HD; Huntington's disease; HRP; horseradish peroxidase;
Longitudinal changes in the fronto-striatal network are associated with executive dysfunction and behavioral dysregulation in Huntington's disease: 30 months IMAGE-HD data
Keywords: بیماری هانتینگتون; Huntington's disease; fMRI; Set shifting; Executive function; Longitudinal;
Simultaneous blockade of NMDA receptors and PARP-1 activity synergistically alleviate immunoexcitotoxicity and bioenergetics in 3-nitropropionic acid intoxicated mice: Evidences from memantine and 3-aminobenzamide interventions
Keywords: بیماری هانتینگتون; 3-Nitropropianic acid; Huntington's disease; Excitotoxicity; NMDA receptors; Bioenergetics; BDNF;
Modulation of proteostasis by transcription factor NRF2 and impact in neurodegenerative diseases
Keywords: بیماری هانتینگتون; α-SYN; alpha synuclein; β-TrCP; β-transducin repeat containing E3 ubiquitin protein ligase; Aβ; amyloid beta; AD; Alzheimer's disease; ALS; amyotrophic lateral sclerosis; AMPK; AMP-activated protein kinase; ARE; antioxidant response element; ASK1; apo
Research PaperSurvival of iPSC-derived grafts within the striatum of immunodeficient mice: Importance of developmental stage of both transplant and host recipient
Keywords: بیماری هانتینگتون; BDNF; brain derived neurotrophic factor; DAPI; 4â²,6-diamidino-2-phenylindole; Dkk1; Dikkopf 1; ESC; embryonic stem cell; GABA; gamma-aminobutyric acid; HD; Huntington's disease; IBSN; infantile bilateral striatal necrosis; iNSC; iPSC-derived neural stem
Motor cortex inhibition by TMS reduces cognitive non-motor procedural learning when immediate incentives are present
Keywords: بیماری هانتینگتون; Continuous theta burst stimulation; Motor cortex; Feedback; Probabilistic classification learning and weather prediction task; AMT; active motor threshold; BG; basal ganglia; cTBS; continuous theta burst stimulation; DLPFC; dorsolateral prefrontal cortex;
Epigenetic and transcriptional modulation of WDR5, a chromatin remodeling protein, in Huntington's disease human induced pluripotent stem cell (hiPSC) model
Keywords: بیماری هانتینگتون; AO; age of onset; CTR; control; DAPI; 4â²,6-Diamidino-2-phenylindole; DMRs; differentially methylated regions; DNAm; DNA methylation; FDR; false discovery rate; gDNA; genomic DNA; GO; gene ontology; HD; Huntington's disease; hESCs; human embryonic stem c
Energy defects in Huntington's disease: Why “in vivo” evidence matters
Keywords: بیماری هانتینگتون; Huntington's disease; NMR; Spectroscopy; Mitochondria; Excitotoxicity; Calcium; Glutamate; NMDA receptors; Energy metabolism; Biomarker;
SMAD transcription factors are altered in cell models of HD and regulate HTT expression
Keywords: بیماری هانتینگتون; Huntington's Disease; Transcription; EGF; TGF-beta; SMAD; Kinase signalling;